ICD10

ICD-10 Code Q87.8: Other specified congenital malformation syndromes, not elsewhere classified

Q87.8 is an ICD-10 diagnosis entry used to group records related to Other specified congenital malformation syndromes, not elsewhere classified. You may see this entry in coding references, medical records, or claims workflows when a broader diagnosis category is being reviewed before a more specific code is chosen. ICD-10 entries help standardize how diagnoses are organized for coding, reporting, analytics, and documentation. This code sits within the broader ICD-10 area for Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA0).

Reviewed by HealthAssure Clinical TeamUpdated 26 May 2026

What is this code?

ICD-10 entries help standardize how diagnoses are organized for coding, reporting, analytics, and documentation. This code sits within the broader ICD-10 area for Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA0).

When is it used?

  • May be used when a clinician documents other specified congenital malformation syndromes, not elsewhere classified in a patient's medical record.
  • May appear in hospital records, claims, referrals, and clinical documentation.
  • This code may act more like a grouping or parent code, so a more specific child code may be used in final documentation when available.

What it does not mean

  • A code alone does not explain severity, treatment plan, or outcome.
  • A medical code should not be treated as a substitute for a doctor's diagnosis or advice.
  • This entry may represent a broader category rather than the most specific billable code.

Code hierarchy

chapter
17Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA0)
block
Q80-Q89Other congenital malformations
category
Q87Other specified congenital malformation syndromes affecting multiple systems
currentQ87

Official coding notes

Excludes1 (do not code together)
  • Zellweger syndrome (E71.510)

Where you may see this code

You may see this entry in coding references, medical records, or claims workflows when a broader diagnosis category is being reviewed before a more specific code is chosen.

Coding guidelines

Compatibility

Legacy code aligns to an official FY 2026 category. Frontend should resolve to the official category page and surface the billable child codes.
Legacy codes
Q87.8
Replacement codes
Q87.81 — Alport syndromeQ87.82 — Arterial tortuosity syndromeQ87.83 — Bardet-Biedl syndromeQ87.84 — Laurence-Moon syndromeQ87.85 — MED13L syndromeQ87.86 — Kleefstra syndromeQ87.87 — Hao-Fountain SyndromeQ87.88 — CTNNB1 syndromeQ87.89 — Other specified congenital malformation syndromes, not elsewhere classified

Common synonyms

Other specified congenital malformation syndromes, not elsewhere classified

Frequently asked questions

Code details

CodeQ87.8
SystemICD10
Display nameOther specified congenital malformation syndromes, not elsewhere classified
ChapterCongenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA0)
BlockOther congenital malformations

Flags

BillableNo
Valid clinical useNo

Source

SourceICD-10
Version2026-annual
Releaseannual
Year2026

About this content

This page is prepared by HealthAssure's clinical team using official coding standards from ICD-10. AI tools assist with drafting explanations, which are then reviewed and verified by healthcare professionals for accuracy. This content is for informational purposes and does not replace professional medical advice. Meet our team.

ICD-10 Code Q87.8 for Other specified congenital malformation syndromes, not elsewhere classified | HealthAssure