ICD10BillableValid for clinical use

ICD-10 Code D47.Z2: Castleman disease

D47.Z2 is a billable ICD-10 diagnosis code used to classify Castleman disease in medical records and claims. You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records. ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Neoplasms (C00-D49).

Reviewed by HealthAssure Clinical TeamUpdated 26 May 2026

What is this code?

ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Neoplasms (C00-D49).

When is it used?

  • May be used when a clinician documents castleman disease in a patient's medical record.
  • May appear in hospital records, claims, referrals, and clinical documentation.
  • This code can be used as a clinically usable diagnosis entry in standardized coding workflows.

What it does not mean

  • A code alone does not explain severity, treatment plan, or outcome.
  • A medical code should not be treated as a substitute for a doctor's diagnosis or advice.

Code hierarchy

chapter
2Neoplasms (C00-D49)
block
D37-D48Neoplasms of uncertain behavior, polycythemia vera and myelodysplastic syndromes
category
D47Other neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue
category
D47.ZOther specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue
currentD47.Z

Official coding notes

Excludes2 (may code together if documented)
  • Kaposi's sarcoma (C46.-)
Code also
  • , if applicable, human herpesvirus 8 infection (B10.89)

Where you may see this code

You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records.

Related specialists

OncologistGeneral Physician

Coding guidelines

Common synonyms

Castleman disease

Frequently asked questions

Code details

CodeD47.Z2
SystemICD10
Display nameCastleman disease
ChapterNeoplasms (C00-D49)
BlockNeoplasms of uncertain behavior, polycythemia vera and myelodysplastic syndromes

Flags

BillableYes
Valid clinical useYes

Source

SourceICD-10
Version2026-annual
Releaseannual
Year2026

Index terms

Matched terms
Disease, diseasedDisease, diseased
See also
Herpesvirus, human, 8

About this content

This page is prepared by HealthAssure's clinical team using official coding standards from ICD-10. AI tools assist with drafting explanations, which are then reviewed and verified by healthcare professionals for accuracy. This content is for informational purposes and does not replace professional medical advice. Meet our team.

ICD-10 Code D47.Z2 for Castleman disease | HealthAssure