ICD10BillableValid for clinical use

ICD-10 Code D80.0: Hereditary hypogammaglobulinemia

D80.0 is a billable ICD-10 diagnosis code used to classify Hereditary hypogammaglobulinemia in medical records and claims. You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records. ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89).

Reviewed by HealthAssure Clinical TeamUpdated 26 May 2026

What is this code?

ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89).

When is it used?

  • May be used when a clinician documents hereditary hypogammaglobulinemia in a patient's medical record.
  • May appear in hospital records, claims, referrals, and clinical documentation.
  • This code can be used as a clinically usable diagnosis entry in standardized coding workflows.

What it does not mean

  • A code alone does not explain severity, treatment plan, or outcome.
  • A medical code should not be treated as a substitute for a doctor's diagnosis or advice.

Code hierarchy

chapter
3Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
block
D80-D89Certain disorders involving the immune mechanism
category
D80Immunodeficiency with predominantly antibody defects
currentD80

Official coding notes

Inclusion terms
  • Autosomal recessive agammaglobulinemia (Swiss type)
  • X-linked agammaglobulinemia [Bruton] (with growth hormone deficiency)

Where you may see this code

You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records.

Related specialists

HematologistGeneral Physician

Mapped diagnoses and classifications

Coding guidelines

Compatibility

Legacy and official ICD code match exactly.
Legacy codes
D80.0

Common synonyms

Hereditary hypogammaglobulinemia

Frequently asked questions

Code details

CodeD80.0
SystemICD10
Display nameHereditary hypogammaglobulinemia
ChapterDiseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
BlockCertain disorders involving the immune mechanism

Flags

BillableYes
Valid clinical useYes

Source

SourceICD-10
Version2026-annual
Releaseannual
Year2026

Index terms

Matched terms
Absence(of) (organ or part) (complete or partial)Agammaglobulinemia(acquired (secondary)) (nonfamilial)Agammaglobulinemia(acquired (secondary)) (nonfamilial)Agammaglobulinemia(acquired (secondary)) (nonfamilial)Agammaglobulinemia(acquired (secondary)) (nonfamilial)Agammaglobulinemia(acquired (secondary)) (nonfamilial)Agammaglobulinemia(acquired (secondary)) (nonfamilial)Bruton's X-linked agammaglobulinemiaDeficiency, deficientHypogammaglobulinemiaImmunodeficiencySyndrome

About this content

This page is prepared by HealthAssure's clinical team using official coding standards from ICD-10. AI tools assist with drafting explanations, which are then reviewed and verified by healthcare professionals for accuracy. This content is for informational purposes and does not replace professional medical advice. Meet our team.

ICD-10 Code D80.0 for Hereditary hypogammaglobulinemia | HealthAssure