ICD10BillableValid for clinical use
ICD-10 Code E00.9: Congenital iodine-deficiency syndrome, unspecified
Reviewed by HealthAssure Clinical TeamUpdated 26 May 2026
What is this code?
ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Endocrine, nutritional and metabolic diseases (E00-E89).
When is it used?
- May be used when a clinician documents congenital iodine-deficiency syndrome, unspecified in a patient's medical record.
- May appear in hospital records, claims, referrals, and clinical documentation.
- This code can be used as a clinically usable diagnosis entry in standardized coding workflows.
What it does not mean
- A code alone does not explain severity, treatment plan, or outcome.
- A medical code should not be treated as a substitute for a doctor's diagnosis or advice.
Code hierarchy
chapter
4Endocrine, nutritional and metabolic diseases (E00-E89)
block
E00-E07Disorders of thyroid gland
category
E00Congenital iodine-deficiency syndrome
currentE00
Official coding notes
Inclusion terms
- Congenital iodine-deficiency hypothyroidism NOS
- Endemic cretinism NOS
Where you may see this code
You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records.
Related specialists
EndocrinologistGeneral Physician
Related codes
Sibling codes
Coverage-related procedures and services
CPT 00532high
ANESTHESIA FOR ACCESS TO CENTRAL VENOUS CIRCULATION
Source: CMS coverage guidance
CPT 01420high
ANESTHESIA FOR ALL CAST APPLICATIONS, REMOVAL, OR REPAIR INVOLVING KNEE JOINT
Source: CMS coverage guidance
CPT 01730high
ANESTHESIA FOR ALL CLOSED PROCEDURES ON HUMERUS AND ELBOW
Source: CMS coverage guidance
CPT 01380high
ANESTHESIA FOR ALL CLOSED PROCEDURES ON KNEE JOINT
Source: CMS coverage guidance
CPT 01820high
ANESTHESIA FOR ALL CLOSED PROCEDURES ON RADIUS, ULNA, WRIST, OR HAND BONES
Source: CMS coverage guidance
CPT 00322high
ANESTHESIA FOR ALL PROCEDURES ON ESOPHAGUS, THYROID, LARYNX, TRACHEA AND LYMPHATIC SYSTEM OF NECK; NEEDLE BIOPSY OF THYROID
Source: CMS coverage guidance
Mapped diagnoses and classifications
SNOMED_CT 722939004high
Congenital hypothyroidism due to iodine deficiency
Source: SNOMED International ICD-10 map
SNOMED_CT 217710005high
Congenital iodine deficiency syndrome
Source: SNOMED International ICD-10 map
SNOMED_CT 75065003high
Endemic cretinism
Source: SNOMED International ICD-10 map
SNOMED_CT 84781002high
Sporadic cretinism
Source: SNOMED International ICD-10 map
Coding guidelines
Compatibility
Legacy and official ICD code match exactly.
Legacy codes
E00.9
Common synonyms
Congenital iodine-deficiency syndrome, unspecifiedCongenital iodine-deficiency syndrome
Frequently asked questions
About this content
This page is prepared by HealthAssure's clinical team using official coding standards from ICD-10. AI tools assist with drafting explanations, which are then reviewed and verified by healthcare professionals for accuracy. This content is for informational purposes and does not replace professional medical advice. Meet our team.