ICD10BillableValid for clinical use
ICD-10 Code E71.2: Disorder of branched-chain amino-acid metabolism, unspecified
Reviewed by HealthAssure Clinical TeamUpdated 26 May 2026
What is this code?
ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Endocrine, nutritional and metabolic diseases (E00-E89).
When is it used?
- May be used when a clinician documents disorder of branched-chain amino-acid metabolism, unspecified in a patient's medical record.
- May appear in hospital records, claims, referrals, and clinical documentation.
- This code can be used as a clinically usable diagnosis entry in standardized coding workflows.
What it does not mean
- A code alone does not explain severity, treatment plan, or outcome.
- A medical code should not be treated as a substitute for a doctor's diagnosis or advice.
Code hierarchy
chapter
4Endocrine, nutritional and metabolic diseases (E00-E89)
block
E70-E88Metabolic disorders
category
E71Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
currentE71
Where you may see this code
You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records.
Related specialists
EndocrinologistGeneral Physician
Related codes
Sibling codes
Mapped diagnoses and classifications
SNOMED_CT 237955004high
Cytosolic acetoacetyl-CoA thiolase deficiency
Source: SNOMED International ICD-10 map
SNOMED_CT 116020001high
Disorder of branched-chain amino acid metabolism
Source: SNOMED International ICD-10 map
SNOMED_CT 24013007high
Hyperleucinemia
Source: SNOMED International ICD-10 map
SNOMED_CT 52270006high
Intermittent branched-chain ketonuria
Source: SNOMED International ICD-10 map
SNOMED_CT 445571008high
Isobutyrylglycinuria
Source: SNOMED International ICD-10 map
SNOMED_CT 237954000high
Mitochondrial 2-methylacetoacetyl-CoA thiolase deficiency - non-potassium stimulated
Source: SNOMED International ICD-10 map
Coding guidelines
Compatibility
Legacy and official ICD code match exactly.
Legacy codes
E71.2
Common synonyms
Disorder of branched-chain amino-acid metabolism, unspecifiedDisorder of branched-chain amino-acid metabolism
Frequently asked questions
About this content
This page is prepared by HealthAssure's clinical team using official coding standards from ICD-10. AI tools assist with drafting explanations, which are then reviewed and verified by healthcare professionals for accuracy. This content is for informational purposes and does not replace professional medical advice. Meet our team.