ICD10
ICD-10 Code E74.0: Glycogen storage disease
Reviewed by HealthAssure Clinical TeamUpdated 26 May 2026
What is this code?
ICD-10 entries help standardize how diagnoses are organized for coding, reporting, analytics, and documentation. This code sits within the broader ICD-10 area for Endocrine, nutritional and metabolic diseases (E00-E89).
When is it used?
- May be used when a clinician documents glycogen storage disease in a patient's medical record.
- May appear in hospital records, claims, referrals, and clinical documentation.
- This code may act more like a grouping or parent code, so a more specific child code may be used in final documentation when available.
What it does not mean
- A code alone does not explain severity, treatment plan, or outcome.
- A medical code should not be treated as a substitute for a doctor's diagnosis or advice.
- This entry may represent a broader category rather than the most specific billable code.
Code hierarchy
chapter
4Endocrine, nutritional and metabolic diseases (E00-E89)
block
E70-E88Metabolic disorders
category
E74Other disorders of carbohydrate metabolism
currentE74
Where you may see this code
You may see this entry in coding references, medical records, or claims workflows when a broader diagnosis category is being reviewed before a more specific code is chosen.
Related specialists
EndocrinologistGeneral Physician
Related codes
Sibling codes
E74.1Disorders of fructose metabolismE74.2Disorders of galactose metabolismE74.3Other disorders of intestinal carbohydrate absorptionE74.4Disorders of pyruvate metabolism and gluconeogenesisbillableE74.8Other specified disorders of carbohydrate metabolismE74.9Disorder of carbohydrate metabolism, unspecifiedbillable
Mapped diagnoses and classifications
SNOMED_CT 721099001high
Adult polyglucosan body disease
Source: SNOMED International ICD-10 map
SNOMED_CT 297253000high
Cardiac glycogen phosphorylase kinase deficiency
Source: SNOMED International ICD-10 map
SNOMED_CT 195025008high
Cardiac glycogenosis
Source: SNOMED International ICD-10 map
SNOMED_CT 419097006high
Danon disease
Source: SNOMED International ICD-10 map
SNOMED_CT 124267007high
Deficiency of 1,4-alpha-glucan branching enzyme
Source: SNOMED International ICD-10 map
SNOMED_CT 124335006high
Deficiency of phosphoglycerate kinase
Source: SNOMED International ICD-10 map
Coding guidelines
Compatibility
Legacy code aligns to an official FY 2026 category. Frontend should resolve to the official category page and surface the billable child codes.
Legacy codes
E74.0
Replacement codes
E74.00 — Glycogen storage disease, unspecifiedE74.01 — von Gierke diseaseE74.02 — Pompe diseaseE74.03 — Cori diseaseE74.04 — McArdle diseaseE74.05 — Lysosome-associated membrane protein 2 [LAMP2] deficiencyE74.09 — Other glycogen storage disease
Common synonyms
Glycogen storage disease
Frequently asked questions
About this content
This page is prepared by HealthAssure's clinical team using official coding standards from ICD-10. AI tools assist with drafting explanations, which are then reviewed and verified by healthcare professionals for accuracy. This content is for informational purposes and does not replace professional medical advice. Meet our team.