ICD10
ICD-10 Code E74.1: Disorders of fructose metabolism
Reviewed by HealthAssure Clinical TeamUpdated 26 May 2026
What is this code?
ICD-10 entries help standardize how diagnoses are organized for coding, reporting, analytics, and documentation. This code sits within the broader ICD-10 area for Endocrine, nutritional and metabolic diseases (E00-E89).
When is it used?
- May be used when a clinician documents disorders of fructose metabolism in a patient's medical record.
- May appear in hospital records, claims, referrals, and clinical documentation.
- This code may act more like a grouping or parent code, so a more specific child code may be used in final documentation when available.
What it does not mean
- A code alone does not explain severity, treatment plan, or outcome.
- A medical code should not be treated as a substitute for a doctor's diagnosis or advice.
- This entry may represent a broader category rather than the most specific billable code.
Code hierarchy
chapter
4Endocrine, nutritional and metabolic diseases (E00-E89)
block
E70-E88Metabolic disorders
category
E74Other disorders of carbohydrate metabolism
currentE74
Official coding notes
Excludes1 (do not code together)
- muscle phosphofructokinase deficiency (E74.09)
Where you may see this code
You may see this entry in coding references, medical records, or claims workflows when a broader diagnosis category is being reviewed before a more specific code is chosen.
Related specialists
EndocrinologistGeneral Physician
Related codes
Sibling codes
E74.0Glycogen storage diseaseE74.2Disorders of galactose metabolismE74.3Other disorders of intestinal carbohydrate absorptionE74.4Disorders of pyruvate metabolism and gluconeogenesisbillableE74.8Other specified disorders of carbohydrate metabolismE74.9Disorder of carbohydrate metabolism, unspecifiedbillable
Mapped diagnoses and classifications
SNOMED_CT 782340001high
Acquired intolerance to fructose
Source: SNOMED International ICD-10 map
SNOMED_CT 124300009high
Deficiency of fructokinase
Source: SNOMED International ICD-10 map
SNOMED_CT 124439001high
Deficiency of fructose-bisphosphatase
Source: SNOMED International ICD-10 map
SNOMED_CT 124299001high
Deficiency of ketohexokinase
Source: SNOMED International ICD-10 map
SNOMED_CT 237977000high
Disorder of glycerol metabolism
Source: SNOMED International ICD-10 map
SNOMED_CT 40278002high
Essential benign fructosuria
Source: SNOMED International ICD-10 map
Coding guidelines
Compatibility
Legacy code aligns to an official FY 2026 category. Frontend should resolve to the official category page and surface the billable child codes.
Legacy codes
E74.1
Replacement codes
E74.10 — Disorder of fructose metabolism, unspecifiedE74.11 — Essential fructosuriaE74.12 — Hereditary fructose intoleranceE74.19 — Other disorders of fructose metabolism
Common synonyms
Disorders of fructose metabolism
Frequently asked questions
About this content
This page is prepared by HealthAssure's clinical team using official coding standards from ICD-10. AI tools assist with drafting explanations, which are then reviewed and verified by healthcare professionals for accuracy. This content is for informational purposes and does not replace professional medical advice. Meet our team.