ICD10
ICD-10 Code E80.2: Other and unspecified porphyria
Reviewed by HealthAssure Clinical TeamUpdated 26 May 2026
What is this code?
ICD-10 entries help standardize how diagnoses are organized for coding, reporting, analytics, and documentation. This code sits within the broader ICD-10 area for Endocrine, nutritional and metabolic diseases (E00-E89).
When is it used?
- May be used when a clinician documents other and unspecified porphyria in a patient's medical record.
- May appear in hospital records, claims, referrals, and clinical documentation.
- This code may act more like a grouping or parent code, so a more specific child code may be used in final documentation when available.
What it does not mean
- A code alone does not explain severity, treatment plan, or outcome.
- A medical code should not be treated as a substitute for a doctor's diagnosis or advice.
- This entry may represent a broader category rather than the most specific billable code.
Code hierarchy
chapter
4Endocrine, nutritional and metabolic diseases (E00-E89)
block
E70-E88Metabolic disorders
category
E80Disorders of porphyrin and bilirubin metabolism
currentE80
Where you may see this code
You may see this entry in coding references, medical records, or claims workflows when a broader diagnosis category is being reviewed before a more specific code is chosen.
Related specialists
EndocrinologistGeneral Physician
Related codes
Sibling codes
E80.0Hereditary erythropoietic porphyriabillableE80.1Porphyria cutanea tardabillableE80.3Defects of catalase and peroxidasebillableE80.4Gilbert syndromebillableE80.5Crigler-Najjar syndromebillableE80.6Other disorders of bilirubin metabolismbillableE80.7Disorder of bilirubin metabolism, unspecifiedbillable
Mapped diagnoses and classifications
SNOMED_CT 234422006high
Acute intermittent porphyria
Source: SNOMED International ICD-10 map
SNOMED_CT 84816006high
Chester-type porphyria
Source: SNOMED International ICD-10 map
SNOMED_CT 190913009high
Congenital porphyria
Source: SNOMED International ICD-10 map
SNOMED_CT 190915002high
Coproporphyria
Source: SNOMED International ICD-10 map
SNOMED_CT 123965000high
Coproporphyrinuria
Source: SNOMED International ICD-10 map
SNOMED_CT 29094004high
Disorder of porphyrin metabolism
Source: SNOMED International ICD-10 map
Coding guidelines
Compatibility
Legacy code aligns to an official FY 2026 category. Frontend should resolve to the official category page and surface the billable child codes.
Legacy codes
E80.2
Replacement codes
E80.20 — Unspecified porphyriaE80.21 — Acute intermittent (hepatic) porphyriaE80.29 — Other porphyria
Common synonyms
Other and unspecified porphyriaOther and porphyria
Frequently asked questions
About this content
This page is prepared by HealthAssure's clinical team using official coding standards from ICD-10. AI tools assist with drafting explanations, which are then reviewed and verified by healthcare professionals for accuracy. This content is for informational purposes and does not replace professional medical advice. Meet our team.