ICD10
ICD-10 Code E88.1: Lipodystrophy, not elsewhere classified
Reviewed by HealthAssure Clinical TeamUpdated 26 May 2026
What is this code?
ICD-10 entries help standardize how diagnoses are organized for coding, reporting, analytics, and documentation. This code sits within the broader ICD-10 area for Endocrine, nutritional and metabolic diseases (E00-E89).
When is it used?
- May be used when a clinician documents lipodystrophy, not elsewhere classified in a patient's medical record.
- May appear in hospital records, claims, referrals, and clinical documentation.
- This code may act more like a grouping or parent code, so a more specific child code may be used in final documentation when available.
What it does not mean
- A code alone does not explain severity, treatment plan, or outcome.
- A medical code should not be treated as a substitute for a doctor's diagnosis or advice.
- This entry may represent a broader category rather than the most specific billable code.
Code hierarchy
chapter
4Endocrine, nutritional and metabolic diseases (E00-E89)
block
E70-E88Metabolic disorders
category
E88Other and unspecified metabolic disorders
currentE88
Official coding notes
Excludes1 (do not code together)
- Whipple's disease (K90.81)
Where you may see this code
You may see this entry in coding references, medical records, or claims workflows when a broader diagnosis category is being reviewed before a more specific code is chosen.
Related specialists
EndocrinologistGeneral Physician
Related codes
Sibling codes
E88.0Disorders of plasma-protein metabolism, not elsewhere classifiedE88.2Lipomatosis, not elsewhere classifiedbillableE88.3Tumor lysis syndromebillableE88.4Mitochondrial metabolism disordersE88.8Other specified metabolic disordersE88.9Metabolic disorder, unspecifiedbillableE88.AWasting disease (syndrome) due to underlying conditionbillable
Mapped diagnoses and classifications
SNOMED_CT 1197746001high
AKT2-related familial partial lipodystrophy
Source: SNOMED International ICD-10 map
SNOMED_CT 86907008high
Acquired generalized lipodystrophy
Source: SNOMED International ICD-10 map
SNOMED_CT 75659004high
Acquired partial lipodystrophy
Source: SNOMED International ICD-10 map
SNOMED_CT 1197747005high
Autosomal semi-dominant severe lipodystrophic laminopathy
Source: SNOMED International ICD-10 map
SNOMED_CT 1197749008high
CIDEC-related familial partial lipodystrophy
Source: SNOMED International ICD-10 map
SNOMED_CT 284449005high
Congenital generalised lipodystrophy
Source: SNOMED International ICD-10 map
Coding guidelines
Compatibility
Legacy code aligns to an official FY 2026 category. Frontend should resolve to the official category page and surface the billable child codes.
Legacy codes
E88.1
Replacement codes
E88.10 — Lipodystrophy, unspecifiedE88.11 — Partial lipodystrophyE88.12 — Generalized lipodystrophyE88.13 — Localized lipodystrophyE88.14 — HIV-associated lipodystrophyE88.19 — Other lipodystrophy, not elsewhere classified
Common synonyms
Lipodystrophy, not elsewhere classified
Frequently asked questions
About this content
This page is prepared by HealthAssure's clinical team using official coding standards from ICD-10. AI tools assist with drafting explanations, which are then reviewed and verified by healthcare professionals for accuracy. This content is for informational purposes and does not replace professional medical advice. Meet our team.