ICD10
ICD-10 Code G11.1: Early-onset cerebellar ataxia
Reviewed by HealthAssure Clinical TeamUpdated 26 May 2026
What is this code?
ICD-10 entries help standardize how diagnoses are organized for coding, reporting, analytics, and documentation. This code sits within the broader ICD-10 area for Diseases of the nervous system (G00-G99).
When is it used?
- May be used when a clinician documents early-onset cerebellar ataxia in a patient's medical record.
- May appear in hospital records, claims, referrals, and clinical documentation.
- This code may act more like a grouping or parent code, so a more specific child code may be used in final documentation when available.
What it does not mean
- A code alone does not explain severity, treatment plan, or outcome.
- A medical code should not be treated as a substitute for a doctor's diagnosis or advice.
- This entry may represent a broader category rather than the most specific billable code.
Code hierarchy
chapter
6Diseases of the nervous system (G00-G99)
block
G10-G14Systemic atrophies primarily affecting the central nervous system
category
G11Hereditary ataxia
currentG11
Where you may see this code
You may see this entry in coding references, medical records, or claims workflows when a broader diagnosis category is being reviewed before a more specific code is chosen.
Related specialists
NeurologistGeneral PhysicianENT Specialist
Related codes
Sibling codes
G11.0Congenital nonprogressive ataxiabillableG11.2Late-onset cerebellar ataxiabillableG11.3Cerebellar ataxia with defective DNA repairbillableG11.4Hereditary spastic paraplegiabillableG11.5Hypomyelination - hypogonadotropic hypogonadism - hypodontiabillableG11.6Leukodystrophy with vanishing white matter diseasebillableG11.8Other hereditary ataxiasbillableG11.9Hereditary ataxia, unspecifiedbillable
Mapped diagnoses and classifications
SNOMED_CT 1187643003high
Acute infantile liver failure, cerebellar ataxia, peripheral sensory motor neuropathy syndrome
Source: SNOMED International ICD-10 map
SNOMED_CT 720517001high
Ataxia with deafness and intellectual disability syndrome
Source: SNOMED International ICD-10 map
SNOMED_CT 783203003high
Ataxia with tapetoretinal degeneration syndrome
Source: SNOMED International ICD-10 map
SNOMED_CT 702442008high
Ataxia with vitamin E deficiency
Source: SNOMED International ICD-10 map
SNOMED_CT 725394006high
Autosomal recessive ataxia due to ubiquinone deficiency
Source: SNOMED International ICD-10 map
SNOMED_CT 1237625002high
Autosomal recessive cerebellar ataxia due to CWF19L1 deficiency
Source: SNOMED International ICD-10 map
Coding guidelines
Compatibility
Legacy code aligns to an official FY 2026 category. Frontend should resolve to the official category page and surface the billable child codes.
Legacy codes
G11.1
Replacement codes
G11.10 — Early-onset cerebellar ataxia, unspecifiedG11.11 — Friedreich ataxiaG11.19 — Other early-onset cerebellar ataxia
Common synonyms
Early-onset cerebellar ataxia
Frequently asked questions
About this content
This page is prepared by HealthAssure's clinical team using official coding standards from ICD-10. AI tools assist with drafting explanations, which are then reviewed and verified by healthcare professionals for accuracy. This content is for informational purposes and does not replace professional medical advice. Meet our team.