ICD10BillableValid for clinical use
ICD-10 Code G23.0: Hallervorden-Spatz disease
Reviewed by HealthAssure Clinical TeamUpdated 26 May 2026
What is this code?
ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Diseases of the nervous system (G00-G99).
When is it used?
- May be used when a clinician documents hallervorden-spatz disease in a patient's medical record.
- May appear in hospital records, claims, referrals, and clinical documentation.
- This code can be used as a clinically usable diagnosis entry in standardized coding workflows.
What it does not mean
- A code alone does not explain severity, treatment plan, or outcome.
- A medical code should not be treated as a substitute for a doctor's diagnosis or advice.
Code hierarchy
chapter
6Diseases of the nervous system (G00-G99)
block
G20-G26Extrapyramidal and movement disorders
category
G23Other degenerative diseases of basal ganglia
currentG23
Official coding notes
Inclusion terms
- Pigmentary pallidal degeneration
Where you may see this code
You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records.
Related specialists
NeurologistGeneral Physician
Related codes
G23.1Progressive supranuclear ophthalmoplegia [Steele-Richardson-Olszewski]codeG23.2Striatonigral degenerationcodeG23.3Hypomyelination with atrophy of the basal ganglia and cerebellumcodeG23.8Other specified degenerative diseases of basal gangliacodeG23.9Degenerative disease of basal ganglia, unspecifiedcode
Sibling codes
G23.1Progressive supranuclear ophthalmoplegia [Steele-Richardson-Olszewski]billableG23.2Striatonigral degenerationbillableG23.3Hypomyelination with atrophy of the basal ganglia and cerebellumbillableG23.8Other specified degenerative diseases of basal gangliabillableG23.9Degenerative disease of basal ganglia, unspecifiedbillable
Coverage-related procedures and services
CPT 95921high
TESTING OF AUTONOMIC NERVOUS SYSTEM FUNCTION; CARDIOVAGAL INNERVATION (PARASYMPATHETIC FUNCTION), INCLUDING 2 OR MORE OF THE FOLLOWING: HEART RATE RESPONSE TO DEEP BREATHING WITH RECORDED R-R INTERVAL, VALSALVA RATIO, AND 30:15 RATIO
Source: CMS coverage guidance
CPT 95924high
TESTING OF AUTONOMIC NERVOUS SYSTEM FUNCTION; COMBINED PARASYMPATHETIC AND SYMPATHETIC ADRENERGIC FUNCTION TESTING WITH AT LEAST 5 MINUTES OF PASSIVE TILT
Source: CMS coverage guidance
CPT 95923high
TESTING OF AUTONOMIC NERVOUS SYSTEM FUNCTION; SUDOMOTOR, INCLUDING 1 OR MORE OF THE FOLLOWING: QUANTITATIVE SUDOMOTOR AXON REFLEX TEST (QSART), SILASTIC SWEAT IMPRINT, THERMOREGULATORY SWEAT TEST, AND CHANGES IN SYMPATHETIC SKIN POTENTIAL
Source: CMS coverage guidance
CPT 95922high
TESTING OF AUTONOMIC NERVOUS SYSTEM FUNCTION; VASOMOTOR ADRENERGIC INNERVATION (SYMPATHETIC ADRENERGIC FUNCTION), INCLUDING BEAT-TO-BEAT BLOOD PRESSURE AND R-R INTERVAL CHANGES DURING VALSALVA MANEUVER AND AT LEAST 5 MINUTES OF PASSIVE TILT
Source: CMS coverage guidance
CPT 92651high
AUDITORY EVOKED POTENTIALS; FOR HEARING STATUS DETERMINATION, BROADBAND STIMULI, WITH INTERPRETATION AND REPORT
Source: CMS coverage guidance
CPT 92652high
AUDITORY EVOKED POTENTIALS; FOR THRESHOLD ESTIMATION AT MULTIPLE FREQUENCIES, WITH INTERPRETATION AND REPORT
Source: CMS coverage guidance
Mapped diagnoses and classifications
SNOMED_CT 1186856001high
Atypical pantothenate kinase associated neurodegeneration
Source: SNOMED International ICD-10 map
SNOMED_CT 732959007high
Beta-propeller protein-associated neurodegeneration
Source: SNOMED International ICD-10 map
SNOMED_CT 1186861004high
Classical pantothenate kinase associated neurodegeneration
Source: SNOMED International ICD-10 map
SNOMED_CT 732264002high
Coenzyme A synthase protein associated neurodegeneration
Source: SNOMED International ICD-10 map
SNOMED_CT 1259679007high
Dementia due to atypical pantothenate kinase associated neurodegeneration
Source: SNOMED International ICD-10 map
SNOMED_CT 1259990004high
Dementia due to classical pantothenate kinase associated neurodegeneration
Source: SNOMED International ICD-10 map
Coding guidelines
Compatibility
Legacy and official ICD code match exactly.
Legacy codes
G23.0
Common synonyms
Hallervorden-Spatz disease
Frequently asked questions
About this content
This page is prepared by HealthAssure's clinical team using official coding standards from ICD-10. AI tools assist with drafting explanations, which are then reviewed and verified by healthcare professionals for accuracy. This content is for informational purposes and does not replace professional medical advice. Meet our team.