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ICD10BillableValid for clinical use

ICD-10 Code G40.42: Cyclin-Dependent Kinase-Like 5 Deficiency Disorder

G40.42 is a billable ICD-10 diagnosis code used to classify Cyclin-Dependent Kinase-Like 5 Deficiency Disorder in medical records and claims. You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records. ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Diseases of the nervous system (G00-G99).

What is this code?

ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Diseases of the nervous system (G00-G99).

When is it used?

  • May be used when a clinician documents cyclin-dependent kinase-like 5 deficiency disorder in a patient's medical record.
  • May appear in hospital records, claims, referrals, and clinical documentation.
  • This code can be used as a clinically usable diagnosis entry in standardized coding workflows.

What it does not mean

  • A code alone does not explain severity, treatment plan, or outcome.
  • A medical code should not be treated as a substitute for a doctor's diagnosis or advice.

Code hierarchy

chapter
6Diseases of the nervous system (G00-G99)
block
G40-G47Episodic and paroxysmal disorders
category
G40Epilepsy and recurrent seizures
category
G40.4Other generalized epilepsy and epileptic syndromes
currentG40.4

Official coding notes

Inclusion terms
  • CDKL5
Applicable to
  • code, if known, to identify associated manifestations, such as:
  • cortical blindness (H47.61-)
  • global developmental delay (F88)
Use additional code
  • code, if known, to identify associated manifestations, such as:
  • cortical blindness (H47.61-)
  • global developmental delay (F88)

Where you may see this code

You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records.

Related specialists

NeurologistGeneral Physician

Coverage-related procedures and services

CPT 96105high
ASSESSMENT OF APHASIA (INCLUDES ASSESSMENT OF EXPRESSIVE AND RECEPTIVE SPEECH AND LANGUAGE FUNCTION, LANGUAGE COMPREHENSION, SPEECH PRODUCTION ABILITY, READING, SPELLING, WRITING, EG, BY BOSTON DIAGNOSTIC APHASIA EXAMINATION) WITH INTERPRETATION AND REPORT, PER HOUR
Source: CMS coverage guidance
CPT 70460high
COMPUTED TOMOGRAPHY, HEAD OR BRAIN; WITH CONTRAST MATERIAL(S)
Source: CMS coverage guidance
CPT 70450high
COMPUTED TOMOGRAPHY, HEAD OR BRAIN; WITHOUT CONTRAST MATERIAL
Source: CMS coverage guidance
CPT 70470high
COMPUTED TOMOGRAPHY, HEAD OR BRAIN; WITHOUT CONTRAST MATERIAL, FOLLOWED BY CONTRAST MATERIAL(S) AND FURTHER SECTIONS
Source: CMS coverage guidance
HCPCS G0451high
DEVELOPMENT TESTING, WITH INTERPRETATION AND REPORT, PER STANDARDIZED INSTRUMENT FORM
Source: CMS coverage guidance
CPT 96113high
DEVELOPMENTAL TEST ADMINISTRATION (INCLUDING ASSESSMENT OF FINE AND/OR GROSS MOTOR, LANGUAGE, COGNITIVE LEVEL, SOCIAL, MEMORY AND/OR EXECUTIVE FUNCTIONS BY STANDARDIZED DEVELOPMENTAL INSTRUMENTS WHEN PERFORMED), BY PHYSICIAN OR OTHER QUALIFIED HEALTH CARE PROFESSIONAL, WITH INTERPRETATION AND REPORT; EACH ADDITIONAL 30 MINUTES (LIST SEPARATELY IN ADDITION TO CODE FOR PRIMARY PROCEDURE)
Source: CMS coverage guidance

Coding guidelines

Common synonyms

Cyclin-Dependent Kinase-Like 5 Deficiency Disorder

Frequently asked questions

Code details

CodeG40.42
SystemICD10
Display nameCyclin-Dependent Kinase-Like 5 Deficiency Disorder
ChapterDiseases of the nervous system (G00-G99)
BlockEpisodic and paroxysmal disorders

Flags

BillableYes
Valid clinical useYes

Source

SourceICD-10
Version2026-annual
Releaseannual
Year2026

Index terms

Matched terms
CDKL5(Cyclin-Dependent Kinase-Like 5 Deficiency Disorder)Disorder(of)

About this content

This page is prepared by HealthAssure's clinical team using official coding standards from ICD-10. AI tools assist with drafting explanations, which are then reviewed and verified by healthcare professionals for accuracy. This content is for informational purposes and does not replace professional medical advice. Meet our team.