ICD10BillableValid for clinical use

ICD-10 Code G71.0342: Limb girdle muscular dystrophy due to beta sarcoglycan dysfunction

G71.0342 is a billable ICD-10 diagnosis code used to classify Limb girdle muscular dystrophy due to beta sarcoglycan dysfunction in medical records and claims. You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records. ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Diseases of the nervous system (G00-G99).

Reviewed by HealthAssure Clinical TeamUpdated 26 May 2026

What is this code?

ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Diseases of the nervous system (G00-G99).

When is it used?

  • May be used when a clinician documents limb girdle muscular dystrophy due to beta sarcoglycan dysfunction in a patient's medical record.
  • May appear in hospital records, claims, referrals, and clinical documentation.
  • This code can be used as a clinically usable diagnosis entry in standardized coding workflows.

What it does not mean

  • A code alone does not explain severity, treatment plan, or outcome.
  • A medical code should not be treated as a substitute for a doctor's diagnosis or advice.

Code hierarchy

chapter
6Diseases of the nervous system (G00-G99)
block
G70-G73Diseases of myoneural junction and muscle
category
G71Primary disorders of muscles
category
G71.0Muscular dystrophy
category
G71.03Limb girdle muscular dystrophies
category
G71.034Limb girdle muscular dystrophy due to sarcoglycan dysfunction
currentG71.034

Official coding notes

Inclusion terms
  • Beta sarcoglycanopathy
  • Limb girdle muscular dystrophy due to beta-sarcoglycan deficiency
  • Limb girdle muscular dystrophy type 2E

Where you may see this code

You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records.

Related specialists

NeurologistGeneral Physician

Coding guidelines

Common synonyms

Limb girdle muscular dystrophy due to beta sarcoglycan dysfunction

Frequently asked questions

Code details

CodeG71.0342
SystemICD10
Display nameLimb girdle muscular dystrophy due to beta sarcoglycan dysfunction
ChapterDiseases of the nervous system (G00-G99)
BlockDiseases of myoneural junction and muscle

Flags

BillableYes
Valid clinical useYes

Source

SourceICD-10
Version2026-annual
Releaseannual
Year2026

Index terms

Matched terms
Dystrophy, dystrophiaDystrophy, dystrophiaDystrophy, dystrophiaDystrophy, dystrophiaSarcoglycanopathy

About this content

This page is prepared by HealthAssure's clinical team using official coding standards from ICD-10. AI tools assist with drafting explanations, which are then reviewed and verified by healthcare professionals for accuracy. This content is for informational purposes and does not replace professional medical advice. Meet our team.

ICD-10 Code G71.0342 for Limb girdle muscular dystrophy due to beta sarcoglycan dysfunction | HealthAssure