ICD10BillableValid for clinical use

ICD-10 Code I01.9: Acute rheumatic heart disease, unspecified

I01.9 is a billable ICD-10 diagnosis code used to classify Acute rheumatic heart disease, unspecified in medical records and claims. You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records. ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Diseases of the circulatory system (I00-I99).

Reviewed by HealthAssure Clinical TeamUpdated 26 May 2026

What is this code?

ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Diseases of the circulatory system (I00-I99).

When is it used?

  • May be used when a clinician documents acute rheumatic heart disease, unspecified in a patient's medical record.
  • May appear in hospital records, claims, referrals, and clinical documentation.
  • This code can be used as a clinically usable diagnosis entry in standardized coding workflows.

What it does not mean

  • A code alone does not explain severity, treatment plan, or outcome.
  • A medical code should not be treated as a substitute for a doctor's diagnosis or advice.

Code hierarchy

chapter
9Diseases of the circulatory system (I00-I99)
block
I00-I02Acute rheumatic fever
category
I01Rheumatic fever with heart involvement
currentI01

Official coding notes

Inclusion terms
  • Any condition in I00 with unspecified type of heart involvement
  • Rheumatic carditis, acute
  • Rheumatic heart disease, active or acute

Where you may see this code

You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records.

Related specialists

CardiologistGeneral PhysicianENT Specialist

Coverage-related procedures and services

CPT 93319high
3D ECHOCARDIOGRAPHIC IMAGING AND POSTPROCESSING DURING TRANSESOPHAGEAL ECHOCARDIOGRAPHY, OR DURING TRANSTHORACIC ECHOCARDIOGRAPHY FOR CONGENITAL CARDIAC ANOMALIES, FOR THE ASSESSMENT OF CARDIAC STRUCTURE(S) (EG, CARDIAC CHAMBERS AND VALVES, LEFT ATRIAL APPENDAGE, INTERATRIAL SEPTUM, INTERVENTRICULAR SEPTUM) AND FUNCTION, WHEN PERFORMED (LIST SEPARATELY IN ADDITION TO CODE FOR ECHOCARDIOGRAPHIC IMAGING)
Source: CMS coverage guidance
CPT 76376high
3D RENDERING WITH INTERPRETATION AND REPORTING OF COMPUTED TOMOGRAPHY, MAGNETIC RESONANCE IMAGING, ULTRASOUND, OR OTHER TOMOGRAPHIC MODALITY WITH IMAGE POSTPROCESSING UNDER CONCURRENT SUPERVISION; NOT REQUIRING IMAGE POSTPROCESSING ON AN INDEPENDENT WORKSTATION
Source: CMS coverage guidance
CPT 76377high
3D RENDERING WITH INTERPRETATION AND REPORTING OF COMPUTED TOMOGRAPHY, MAGNETIC RESONANCE IMAGING, ULTRASOUND, OR OTHER TOMOGRAPHIC MODALITY WITH IMAGE POSTPROCESSING UNDER CONCURRENT SUPERVISION; REQUIRING IMAGE POSTPROCESSING ON AN INDEPENDENT WORKSTATION
Source: CMS coverage guidance
CPT 93325high
DOPPLER ECHOCARDIOGRAPHY COLOR FLOW VELOCITY MAPPING (LIST SEPARATELY IN ADDITION TO CODES FOR ECHOCARDIOGRAPHY)
Source: CMS coverage guidance
CPT 93320high
DOPPLER ECHOCARDIOGRAPHY, PULSED WAVE AND/OR CONTINUOUS WAVE WITH SPECTRAL DISPLAY (LIST SEPARATELY IN ADDITION TO CODES FOR ECHOCARDIOGRAPHIC IMAGING); COMPLETE
Source: CMS coverage guidance
CPT 93321high
DOPPLER ECHOCARDIOGRAPHY, PULSED WAVE AND/OR CONTINUOUS WAVE WITH SPECTRAL DISPLAY (LIST SEPARATELY IN ADDITION TO CODES FOR ECHOCARDIOGRAPHIC IMAGING); FOLLOW-UP OR LIMITED STUDY (LIST SEPARATELY IN ADDITION TO CODES FOR ECHOCARDIOGRAPHIC IMAGING)
Source: CMS coverage guidance

Coding guidelines

Compatibility

Legacy and official ICD code match exactly.
Legacy codes
I01.9

Common synonyms

Acute rheumatic heart disease, unspecifiedAcute rheumatic heart disease

Frequently asked questions

Code details

CodeI01.9
SystemICD10
Display nameAcute rheumatic heart disease, unspecified
ChapterDiseases of the circulatory system (I00-I99)
BlockAcute rheumatic fever

Flags

BillableYes
Valid clinical useYes

Source

SourceICD-10
Version2026-annual
Releaseannual
Year2026

Index terms

Matched terms
Bouillaud's disease or syndrome(rheumatic heart disease)Disease, diseasedDisease, diseasedDisease, diseasedSyndrome

About this content

This page is prepared by HealthAssure's clinical team using official coding standards from ICD-10. AI tools assist with drafting explanations, which are then reviewed and verified by healthcare professionals for accuracy. This content is for informational purposes and does not replace professional medical advice. Meet our team.

ICD-10 Code I01.9 for Acute rheumatic heart disease, unspecified | HealthAssure