ICD10BillableValid for clinical use

ICD-10 Code I27.841: Fontan-associated lymphatic dysfunction

I27.841 is a billable ICD-10 diagnosis code used to classify Fontan-associated lymphatic dysfunction in medical records and claims. You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records. ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Diseases of the circulatory system (I00-I99).

Reviewed by HealthAssure Clinical TeamUpdated 26 May 2026

What is this code?

ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Diseases of the circulatory system (I00-I99).

When is it used?

  • May be used when a clinician documents fontan-associated lymphatic dysfunction in a patient's medical record.
  • May appear in hospital records, claims, referrals, and clinical documentation.
  • This code can be used as a clinically usable diagnosis entry in standardized coding workflows.

What it does not mean

  • A code alone does not explain severity, treatment plan, or outcome.
  • A medical code should not be treated as a substitute for a doctor's diagnosis or advice.

Code hierarchy

chapter
9Diseases of the circulatory system (I00-I99)
block
I26-I28Pulmonary heart disease and diseases of pulmonary circulation
category
I27Other pulmonary heart diseases
category
I27.8Other specified pulmonary heart diseases
category
I27.84Fontan related circulation
currentI27.84

Official coding notes

Code also
  • associated conditions such as:
  • chylothorax (J94.0)
  • Fontan associated protein-losing enteropathy (K90.89)
  • plastic (obstructive) bronchitis (J44.89)

Where you may see this code

You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records.

Related specialists

CardiologistGeneral Physician

Coverage-related procedures and services

CPT 31720high
CATHETER ASPIRATION (SEPARATE PROCEDURE); NASOTRACHEAL
Source: CMS coverage guidance
CPT 94664high
DEMONSTRATION AND/OR EVALUATION OF PATIENT UTILIZATION OF AN AEROSOL GENERATOR, NEBULIZER, METERED DOSE INHALER OR IPPB DEVICE
Source: CMS coverage guidance
CPT 94640high
PRESSURIZED OR NONPRESSURIZED INHALATION TREATMENT FOR ACUTE AIRWAY OBSTRUCTION FOR THERAPEUTIC PURPOSES AND/OR FOR DIAGNOSTIC PURPOSES SUCH AS SPUTUM INDUCTION WITH AN AEROSOL GENERATOR, NEBULIZER, METERED DOSE INHALER OR INTERMITTENT POSITIVE PRESSURE BREATHING (IPPB) DEVICE
Source: CMS coverage guidance
CPT 94642high
AEROSOL INHALATION OF PENTAMIDINE FOR PNEUMOCYSTIS CARINII PNEUMONIA TREATMENT OR PROPHYLAXIS
Source: CMS coverage guidance
CPT 94728high
AIRWAY RESISTANCE BY OSCILLOMETRY
Source: CMS coverage guidance
CPT 94450high
BREATHING RESPONSE TO HYPOXIA (HYPOXIA RESPONSE CURVE)
Source: CMS coverage guidance

Coding guidelines

Common synonyms

Fontan-associated lymphatic dysfunction

Frequently asked questions

Code details

CodeI27.841
SystemICD10
Display nameFontan-associated lymphatic dysfunction
ChapterDiseases of the circulatory system (I00-I99)
BlockPulmonary heart disease and diseases of pulmonary circulation

Flags

BillableYes
Valid clinical useYes

Source

SourceICD-10
Version2026-annual
Releaseannual
Year2026

Index terms

Matched terms
CirculationDysfunction

About this content

This page is prepared by HealthAssure's clinical team using official coding standards from ICD-10. AI tools assist with drafting explanations, which are then reviewed and verified by healthcare professionals for accuracy. This content is for informational purposes and does not replace professional medical advice. Meet our team.

ICD-10 Code I27.841 for Fontan-associated lymphatic dysfunction | HealthAssure