ICD10BillableValid for clinical use
ICD-10 Code I42.9: Cardiomyopathy, unspecified
Reviewed by HealthAssure Clinical TeamUpdated 26 May 2026
What is this code?
ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Diseases of the circulatory system (I00-I99).
When is it used?
- May be used when a clinician documents cardiomyopathy, unspecified in a patient's medical record.
- May appear in hospital records, claims, referrals, and clinical documentation.
- This code can be used as a clinically usable diagnosis entry in standardized coding workflows.
What it does not mean
- A code alone does not explain severity, treatment plan, or outcome.
- A medical code should not be treated as a substitute for a doctor's diagnosis or advice.
Code hierarchy
chapter
9Diseases of the circulatory system (I00-I99)
block
I30-I5AOther forms of heart disease
category
I42Cardiomyopathy
currentI42
Official coding notes
Inclusion terms
- Cardiomyopathy (primary) (secondary) NOS
Where you may see this code
You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records.
Related specialists
CardiologistGeneral Physician
Related codes
I42.0Dilated cardiomyopathycodeI42.1Obstructive hypertrophic cardiomyopathycodeI42.2Other hypertrophic cardiomyopathycodeI42.3Endomyocardial (eosinophilic) diseasecodeI42.4Endocardial fibroelastosiscodeI42.5Other restrictive cardiomyopathycodeI42.6Alcoholic cardiomyopathycodeI42.7Cardiomyopathy due to drug and external agentcodeI42.8Other cardiomyopathiescode
Sibling codes
I42.0Dilated cardiomyopathybillableI42.1Obstructive hypertrophic cardiomyopathybillableI42.2Other hypertrophic cardiomyopathybillableI42.3Endomyocardial (eosinophilic) diseasebillableI42.4Endocardial fibroelastosisbillableI42.5Other restrictive cardiomyopathybillableI42.6Alcoholic cardiomyopathybillableI42.7Cardiomyopathy due to drug and external agentbillableI42.8Other cardiomyopathiesbillable
Coverage-related procedures and services
CPT 93319high
3D ECHOCARDIOGRAPHIC IMAGING AND POSTPROCESSING DURING TRANSESOPHAGEAL ECHOCARDIOGRAPHY, OR DURING TRANSTHORACIC ECHOCARDIOGRAPHY FOR CONGENITAL CARDIAC ANOMALIES, FOR THE ASSESSMENT OF CARDIAC STRUCTURE(S) (EG, CARDIAC CHAMBERS AND VALVES, LEFT ATRIAL APPENDAGE, INTERATRIAL SEPTUM, INTERVENTRICULAR SEPTUM) AND FUNCTION, WHEN PERFORMED (LIST SEPARATELY IN ADDITION TO CODE FOR ECHOCARDIOGRAPHIC IMAGING)
Source: CMS coverage guidance
CPT 93325high
DOPPLER ECHOCARDIOGRAPHY COLOR FLOW VELOCITY MAPPING (LIST SEPARATELY IN ADDITION TO CODES FOR ECHOCARDIOGRAPHY)
Source: CMS coverage guidance
CPT 93355high
ECHOCARDIOGRAPHY, TRANSESOPHAGEAL (TEE) FOR GUIDANCE OF A TRANSCATHETER INTRACARDIAC OR GREAT VESSEL(S) STRUCTURAL INTERVENTION(S) (EG, TAVR, TRANSCATHETER PULMONARY VALVE REPLACEMENT, MITRAL VALVE REPAIR, PARAVALVULAR REGURGITATION REPAIR, LEFT ATRIAL APPENDAGE OCCLUSION/CLOSURE, VENTRICULAR SEPTAL DEFECT CLOSURE) (PERI-AND INTRA-PROCEDURAL), REAL-TIME IMAGE ACQUISITION AND DOCUMENTATION, GUIDANCE WITH QUANTITATIVE MEASUREMENTS, PROBE MANIPULATION, INTERPRETATION, AND REPORT, INCLUDING DIAGNOSTIC TRANSESOPHAGEAL ECHOCARDIOGRAPHY AND, WHEN PERFORMED, ADMINISTRATION OF ULTRASOUND CONTRAST, DOPPLER, COLOR FLOW, AND 3D
Source: CMS coverage guidance
CPT 93318high
ECHOCARDIOGRAPHY, TRANSESOPHAGEAL (TEE) FOR MONITORING PURPOSES, INCLUDING PROBE PLACEMENT, REAL TIME 2-DIMENSIONAL IMAGE ACQUISITION AND INTERPRETATION LEADING TO ONGOING (CONTINUOUS) ASSESSMENT OF (DYNAMICALLY CHANGING) CARDIAC PUMPING FUNCTION AND TO THERAPEUTIC MEASURES ON AN IMMEDIATE TIME BASIS
Source: CMS coverage guidance
CPT 93314high
ECHOCARDIOGRAPHY, TRANSESOPHAGEAL, REAL-TIME WITH IMAGE DOCUMENTATION (2D) (WITH OR WITHOUT M-MODE RECORDING); IMAGE ACQUISITION, INTERPRETATION AND REPORT ONLY
Source: CMS coverage guidance
CPT 93312high
ECHOCARDIOGRAPHY, TRANSESOPHAGEAL, REAL-TIME WITH IMAGE DOCUMENTATION (2D) (WITH OR WITHOUT M-MODE RECORDING); INCLUDING PROBE PLACEMENT, IMAGE ACQUISITION, INTERPRETATION AND REPORT
Source: CMS coverage guidance
Mapped diagnoses and classifications
SNOMED_CT 1186866009high
Acromegalic cardiomyopathy
Source: SNOMED International ICD-10 map
SNOMED_CT 85898001high
Cardiomyopathy
Source: SNOMED International ICD-10 map
SNOMED_CT 713523008high
Cardiomyopathy co-occurrent with human immunodeficiency virus infection
Source: SNOMED International ICD-10 map
SNOMED_CT 860837007high
Cardiomyopathy due to connective tissue disease
Source: SNOMED International ICD-10 map
SNOMED_CT 471846004high
Cardiomyopathy due to neuromuscular disorder
Source: SNOMED International ICD-10 map
SNOMED_CT 471863000high
Disorder of myocardium due to sickle cell hemoglobinopathy
Source: SNOMED International ICD-10 map
Coding guidelines
Compatibility
Legacy and official ICD code match exactly.
Legacy codes
I42.9
Common synonyms
Cardiomyopathy, unspecifiedCardiomyopathy
Frequently asked questions
About this content
This page is prepared by HealthAssure's clinical team using official coding standards from ICD-10. AI tools assist with drafting explanations, which are then reviewed and verified by healthcare professionals for accuracy. This content is for informational purposes and does not replace professional medical advice. Meet our team.