ICD10BillableValid for clinical use
ICD-10 Code K00.5: Hereditary disturbances in tooth structure, not elsewhere classified
Reviewed by HealthAssure Clinical TeamUpdated 26 May 2026
What is this code?
ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Diseases of the digestive system (K00-K95).
When is it used?
- May be used when a clinician documents hereditary disturbances in tooth structure, not elsewhere classified in a patient's medical record.
- May appear in hospital records, claims, referrals, and clinical documentation.
- This code can be used as a clinically usable diagnosis entry in standardized coding workflows.
What it does not mean
- A code alone does not explain severity, treatment plan, or outcome.
- A medical code should not be treated as a substitute for a doctor's diagnosis or advice.
Code hierarchy
chapter
11Diseases of the digestive system (K00-K95)
block
K00-K14Diseases of oral cavity and salivary glands
category
K00Disorders of tooth development and eruption
currentK00
Official coding notes
Inclusion terms
- Amelogenesis imperfecta
- Dentinogenesis imperfecta
- Odontogenesis imperfecta
- Dentinal dysplasia
- Shell teeth
Where you may see this code
You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records.
Related specialists
GastroenterologistGeneral Physician
Related codes
K00.0AnodontiacodeK00.1Supernumerary teethcodeK00.2Abnormalities of size and form of teethcodeK00.3Mottled teethcodeK00.4Disturbances in tooth formationcodeK00.6Disturbances in tooth eruptioncodeK00.7Teething syndromecodeK00.8Other disorders of tooth developmentcodeK00.9Disorder of tooth development, unspecifiedcode
Sibling codes
K00.0AnodontiabillableK00.1Supernumerary teethbillableK00.2Abnormalities of size and form of teethbillableK00.3Mottled teethbillableK00.4Disturbances in tooth formationbillableK00.6Disturbances in tooth eruptionbillableK00.7Teething syndromebillableK00.8Other disorders of tooth developmentbillableK00.9Disorder of tooth development, unspecifiedbillable
Mapped diagnoses and classifications
SNOMED_CT 78494001high
Amelogenesis imperfecta
Source: SNOMED International ICD-10 map
SNOMED_CT 234965004high
Amelogenesis imperfecta - hypomaturation - recessive pigmented
Source: SNOMED International ICD-10 map
SNOMED_CT 234966003high
Amelogenesis imperfecta - hypomaturation - snow capped teeth
Source: SNOMED International ICD-10 map
SNOMED_CT 234961008high
Amelogenesis imperfecta - hypoplastic autosomal dominant - local
Source: SNOMED International ICD-10 map
SNOMED_CT 234963006high
Amelogenesis imperfecta - hypoplastic autosomal dominant - rough
Source: SNOMED International ICD-10 map
SNOMED_CT 234962001high
Amelogenesis imperfecta - hypoplastic autosomal dominant - smooth
Source: SNOMED International ICD-10 map
Coding guidelines
Compatibility
Legacy and official ICD code match exactly.
Legacy codes
K00.5
Common synonyms
Hereditary disturbances in tooth structure, not elsewhere classified
Frequently asked questions
About this content
This page is prepared by HealthAssure's clinical team using official coding standards from ICD-10. AI tools assist with drafting explanations, which are then reviewed and verified by healthcare professionals for accuracy. This content is for informational purposes and does not replace professional medical advice. Meet our team.