ICD10BillableValid for clinical use

ICD-10 Code M04.8: Other autoinflammatory syndromes

M04.8 is a billable ICD-10 diagnosis code used to classify Other autoinflammatory syndromes in medical records and claims. You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records. ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Diseases of the musculoskeletal system and connective tissue (M00-M99).

Reviewed by HealthAssure Clinical TeamUpdated 21 May 2026

What is this code?

ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Diseases of the musculoskeletal system and connective tissue (M00-M99).

When is it used?

  • May be used when a clinician documents other autoinflammatory syndromes in a patient's medical record.
  • May appear in hospital records, claims, referrals, and clinical documentation.
  • This code can be used as a clinically usable diagnosis entry in standardized coding workflows.

What it does not mean

  • A code alone does not explain severity, treatment plan, or outcome.
  • A medical code should not be treated as a substitute for a doctor's diagnosis or advice.

Code hierarchy

chapter
13Diseases of the musculoskeletal system and connective tissue (M00-M99)
block
M00-M25Arthropathies
block
M04Autoinflammatory syndromes (M04)
category
M04Autoinflammatory syndromes
currentM04

Official coding notes

Inclusion terms
  • Blau syndrome
  • Deficiency of interleukin 1 receptor antagonist [DIRA]
  • Majeed syndrome
  • Periodic fever, aphthous stomatitis, pharyngitis, and adenopathy syndrome [PFAPA]
  • Pyogenic arthritis, pyoderma gangrenosum, and acne syndrome [PAPA]

Where you may see this code

You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records.

Related specialists

Orthopedic SpecialistRheumatologist

Coding guidelines

Common synonyms

Other autoinflammatory syndromes

Frequently asked questions

Code details

CodeM04.8
SystemICD10
Display nameOther autoinflammatory syndromes
ChapterDiseases of the musculoskeletal system and connective tissue (M00-M99)
BlockAutoinflammatory syndromes (M04)

Flags

BillableYes
Valid clinical useYes

Source

SourceICD-10
Version2026-annual
Releaseannual
Year2026

Index terms

Matched terms
DIRA(deficiency of interleukin 1 receptor antagonist)Deficiency, deficientDisease, diseasedDisease, diseasedPAPA(pyogenic arthritis, pyoderma gangrenosum, and acne syndrome)PFAPA(periodic fever, aphthous stomatitis, pharyngitis, and adenopathy syndrome)SyndromeSyndromeSyndromeSyndromeSyndromeSyndrome

About this content

This page is prepared by HealthAssure's clinical team using official coding standards from ICD-10. AI tools assist with drafting explanations, which are then reviewed and verified by healthcare professionals for accuracy. This content is for informational purposes and does not replace professional medical advice. Meet our team.

ICD-10 Code M04.8 for Other autoinflammatory syndromes | HealthAssure