What does ICD-10 code N00 mean?

ICD-10 code N00 is the standardized code used for acute nephritic syndrome in medical records and coding systems.

When is ICD-10 code N00 used?

Doctors, hospitals, and insurers may use ICD-10 code N00 when recording acute nephritic syndrome in a standardized format. This entry may also act as a broader category that points toward more specific child codes.

Does ICD-10 code N00 confirm a diagnosis?

No. A code helps standardize documentation and claims, but it should not be read as a substitute for a clinician's full assessment.

ICD10

ICD-10 Code N00: Acute nephritic syndrome

Name: ICD-10 Code N00: Acute nephritic syndrome
Creator: HealthAssure Clinical Team
Published: 2026-05-21T06:26:12.642Z

N00 is an ICD-10 diagnosis entry used to group records related to Acute nephritic syndrome. You may see this entry in coding references, medical records, or claims workflows when a broader diagnosis category is being reviewed before a more specific code is chosen. ICD-10 entries help standardize how diagnoses are organized for coding, reporting, analytics, and documentation. This code sits within the broader ICD-10 area for Diseases of the genitourinary system (N00-N99).

Reviewed by HealthAssure Clinical TeamUpdated 21 May 2026

What is this code?

ICD-10 entries help standardize how diagnoses are organized for coding, reporting, analytics, and documentation. This code sits within the broader ICD-10 area for Diseases of the genitourinary system (N00-N99).

When is it used?

May be used when a clinician documents acute nephritic syndrome in a patient's medical record.
May appear in hospital records, claims, referrals, and clinical documentation.
This code may act more like a grouping or parent code, so a more specific child code may be used in final documentation when available.

What it does not mean

A code alone does not explain severity, treatment plan, or outcome.
A medical code should not be treated as a substitute for a doctor's diagnosis or advice.
This entry may represent a broader category rather than the most specific billable code.

Code hierarchy

chapter

14Diseases of the genitourinary system (N00-N99)

block

N00-N08Glomerular diseases

currentN00-N08

Official coding notes

Includes

acute glomerular disease
acute glomerulonephritis
acute nephritis

Excludes1 (do not code together)

acute tubulo-interstitial nephritis (N10)
nephritic syndrome NOS (N05.-)

Where you may see this code

You may see this entry in coding references, medical records, or claims workflows when a broader diagnosis category is being reviewed before a more specific code is chosen.

Related specialists

UrologistGynecologist

Sibling codes

N01Rapidly progressive nephritic syndrome N02Recurrent and persistent hematuria N03Chronic nephritic syndrome N04Nephrotic syndrome N05Unspecified nephritic syndrome N06Isolated proteinuria with specified morphological lesion N07Hereditary nephropathy, not elsewhere classified N08Glomerular disorders in diseases classified elsewherebillable

Coding guidelines

Compatibility

Legacy code aligns to an official FY 2026 category. Frontend should resolve to the official category page and surface the billable child codes.

Legacy codes

N00

Replacement codes

N00.0 — Acute nephritic syndrome with minor glomerular abnormalityN00.1 — Acute nephritic syndrome with focal and segmental glomerular lesionsN00.2 — Acute nephritic syndrome with diffuse membranous glomerulonephritisN00.3 — Acute nephritic syndrome with diffuse mesangial proliferative glomerulonephritisN00.4 — Acute nephritic syndrome with diffuse endocapillary proliferative glomerulonephritisN00.5 — Acute nephritic syndrome with diffuse mesangiocapillary glomerulonephritisN00.6 — Acute nephritic syndrome with dense deposit diseaseN00.7 — Acute nephritic syndrome with diffuse crescentic glomerulonephritisN00.8 — Acute nephritic syndrome with other morphologic changesN00.9 — Acute nephritic syndrome with unspecified morphologic changesN00.A — Acute nephritic syndrome with C3 glomerulonephritis

Common synonyms

Acute nephritic syndrome

Frequently asked questions

About this content

This page is prepared by HealthAssure's clinical team using official coding standards from ICD-10. AI tools assist with drafting explanations, which are then reviewed and verified by healthcare professionals for accuracy. This content is for informational purposes and does not replace professional medical advice. Meet our team.