ICD10

ICD-10 Code Q03: Congenital hydrocephalus

Q03 is an ICD-10 diagnosis entry used to group records related to Congenital hydrocephalus. You may see this entry in coding references, medical records, or claims workflows when a broader diagnosis category is being reviewed before a more specific code is chosen. ICD-10 entries help standardize how diagnoses are organized for coding, reporting, analytics, and documentation. This code sits within the broader ICD-10 area for Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA0).

Reviewed by HealthAssure Clinical TeamUpdated 21 May 2026

What is this code?

ICD-10 entries help standardize how diagnoses are organized for coding, reporting, analytics, and documentation. This code sits within the broader ICD-10 area for Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA0).

When is it used?

  • May be used when a clinician documents congenital hydrocephalus in a patient's medical record.
  • May appear in hospital records, claims, referrals, and clinical documentation.
  • This code may act more like a grouping or parent code, so a more specific child code may be used in final documentation when available.

What it does not mean

  • A code alone does not explain severity, treatment plan, or outcome.
  • A medical code should not be treated as a substitute for a doctor's diagnosis or advice.
  • This entry may represent a broader category rather than the most specific billable code.

Code hierarchy

chapter
17Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA0)
block
Q00-Q07Congenital malformations of the nervous system
currentQ00-Q07

Official coding notes

Includes
  • hydrocephalus in newborn
Excludes1 (do not code together)
  • Arnold-Chiari syndrome, type II (Q07.0-)
  • acquired hydrocephalus (G91.-)
  • hydrocephalus due to congenital toxoplasmosis (P37.1)
  • hydrocephalus with spina bifida (Q05.0-Q05.4)

Where you may see this code

You may see this entry in coding references, medical records, or claims workflows when a broader diagnosis category is being reviewed before a more specific code is chosen.

Coding guidelines

Compatibility

Legacy code aligns to an official FY 2026 category. Frontend should resolve to the official category page and surface the billable child codes.
Legacy codes
Q03
Replacement codes
Q03.0 — Malformations of aqueduct of SylviusQ03.1 — Atresia of foramina of Magendie and LuschkaQ03.8 — Other congenital hydrocephalusQ03.9 — Congenital hydrocephalus, unspecified

Common synonyms

Congenital hydrocephalus

Frequently asked questions

Code details

CodeQ03
SystemICD10
Display nameCongenital hydrocephalus
ChapterCongenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA0)
BlockCongenital malformations of the nervous system

Flags

BillableNo
Valid clinical useNo

Source

SourceICD-10
Version2026-annual
Releaseannual
Year2026

About this content

This page is prepared by HealthAssure's clinical team using official coding standards from ICD-10. AI tools assist with drafting explanations, which are then reviewed and verified by healthcare professionals for accuracy. This content is for informational purposes and does not replace professional medical advice. Meet our team.