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ICD10BillableValid for clinical use

ICD-10 Code Q22.5: Ebstein's anomaly

Q22.5 is a billable ICD-10 diagnosis code used to classify Ebstein's anomaly in medical records and claims. You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records. ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA0).

Reviewed by HealthAssure Clinical TeamUpdated 26 May 2026

What is this code?

ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA0).

When is it used?

  • May be used when a clinician documents ebstein's anomaly in a patient's medical record.
  • May appear in hospital records, claims, referrals, and clinical documentation.
  • This code can be used as a clinically usable diagnosis entry in standardized coding workflows.

What it does not mean

  • A code alone does not explain severity, treatment plan, or outcome.
  • A medical code should not be treated as a substitute for a doctor's diagnosis or advice.

Code hierarchy

chapter
17Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA0)
block
Q20-Q28Congenital malformations of the circulatory system
category
Q22Congenital malformations of pulmonary and tricuspid valves
currentQ22

Where you may see this code

You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records.

Coverage-related procedures and services

CPT 75574high
COMPUTED TOMOGRAPHIC ANGIOGRAPHY, HEART, CORONARY ARTERIES AND BYPASS GRAFTS (WHEN PRESENT), WITH CONTRAST MATERIAL, INCLUDING 3D IMAGE POSTPROCESSING (INCLUDING EVALUATION OF CARDIAC STRUCTURE AND MORPHOLOGY, ASSESSMENT OF CARDIAC FUNCTION, AND EVALUATION OF VENOUS STRUCTURES, IF PERFORMED)
Source: CMS coverage guidance
CPT 75572high
COMPUTED TOMOGRAPHY, HEART, WITH CONTRAST MATERIAL, FOR EVALUATION OF CARDIAC STRUCTURE AND MORPHOLOGY (INCLUDING 3D IMAGE POSTPROCESSING, ASSESSMENT OF CARDIAC FUNCTION, AND EVALUATION OF VENOUS STRUCTURES, IF PERFORMED)
Source: CMS coverage guidance
CPT 75573high
COMPUTED TOMOGRAPHY, HEART, WITH CONTRAST MATERIAL, FOR EVALUATION OF CARDIAC STRUCTURE AND MORPHOLOGY IN THE SETTING OF CONGENITAL HEART DISEASE (INCLUDING 3D IMAGE POSTPROCESSING, ASSESSMENT OF LEFT VENTRICULAR [LV] CARDIAC FUNCTION, RIGHT VENTRICULAR [RV] STRUCTURE AND FUNCTION AND EVALUATION OF VASCULAR STRUCTURES, IF PERFORMED)
Source: CMS coverage guidance
CPT 93325high
DOPPLER ECHOCARDIOGRAPHY COLOR FLOW VELOCITY MAPPING (LIST SEPARATELY IN ADDITION TO CODES FOR ECHOCARDIOGRAPHY)
Source: CMS coverage guidance
CPT 93320high
DOPPLER ECHOCARDIOGRAPHY, PULSED WAVE AND/OR CONTINUOUS WAVE WITH SPECTRAL DISPLAY (LIST SEPARATELY IN ADDITION TO CODES FOR ECHOCARDIOGRAPHIC IMAGING); COMPLETE
Source: CMS coverage guidance
CPT 93321high
DOPPLER ECHOCARDIOGRAPHY, PULSED WAVE AND/OR CONTINUOUS WAVE WITH SPECTRAL DISPLAY (LIST SEPARATELY IN ADDITION TO CODES FOR ECHOCARDIOGRAPHIC IMAGING); FOLLOW-UP OR LIMITED STUDY (LIST SEPARATELY IN ADDITION TO CODES FOR ECHOCARDIOGRAPHIC IMAGING)
Source: CMS coverage guidance

Mapped diagnoses and classifications

SNOMED_CT 1382053008high
Ebstein anomaly of tricuspid valve with circular shunt originating during fetal period
Source: SNOMED International ICD-10 map
SNOMED_CT 1381885005high
Ebstein anomaly of tricuspid valve with functional pulmonary valve atresia
Source: SNOMED International ICD-10 map
SNOMED_CT 204357006high
Ebstein's anomaly
Source: SNOMED International ICD-10 map
SNOMED_CT 449086000high
Ebstein's anomaly of left atrioventricular valve in functionally univentricular heart
Source: SNOMED International ICD-10 map
SNOMED_CT 447915002high
Ebstein's anomaly of left sided tricuspid valve with discordant atrioventricular connections
Source: SNOMED International ICD-10 map
SNOMED_CT 449087009high
Ebstein's anomaly of right atrioventricular valve in functionally univentricular heart
Source: SNOMED International ICD-10 map

Coding guidelines

Compatibility

Legacy and official ICD code match exactly.
Legacy codes
Q22.5

Common synonyms

Ebstein's anomaly

Frequently asked questions

Code details

CodeQ22.5
SystemICD10
Display nameEbstein's anomaly
ChapterCongenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA0)
BlockCongenital malformations of the circulatory system

Flags

BillableYes
Valid clinical useYes

Source

SourceICD-10
Version2026-annual
Releaseannual
Year2026

Index terms

Matched terms
Abnormal, abnormality, abnormalitiesAnomaly, anomalous(congenital) (unspecified type)Anomaly, anomalous(congenital) (unspecified type)DeformityDisease, diseasedEbstein's anomaly or syndrome(heart)Syndrome

About this content

This page is prepared by HealthAssure's clinical team using official coding standards from ICD-10. AI tools assist with drafting explanations, which are then reviewed and verified by healthcare professionals for accuracy. This content is for informational purposes and does not replace professional medical advice. Meet our team.

ICD-10 Code Q22.5 for Ebstein's anomaly | HealthAssure