ICD10BillableValid for clinical use

ICD-10 Code Q87.42: Marfan syndrome with ocular manifestations

Q87.42 is a billable ICD-10 diagnosis code used to classify Marfan syndrome with ocular manifestations in medical records and claims. You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records. ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA0).

Reviewed by HealthAssure Clinical TeamUpdated 26 May 2026

What is this code?

ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA0).

When is it used?

  • May be used when a clinician documents marfan syndrome with ocular manifestations in a patient's medical record.
  • May appear in hospital records, claims, referrals, and clinical documentation.
  • This code can be used as a clinically usable diagnosis entry in standardized coding workflows.

What it does not mean

  • A code alone does not explain severity, treatment plan, or outcome.
  • A medical code should not be treated as a substitute for a doctor's diagnosis or advice.

Code hierarchy

chapter
17Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA0)
block
Q80-Q89Other congenital malformations
category
Q87Other specified congenital malformation syndromes affecting multiple systems
category
Q87.4Marfan syndrome
currentQ87.4

Where you may see this code

You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records.

Coverage-related procedures and services

CPT 93325high
DOPPLER ECHOCARDIOGRAPHY COLOR FLOW VELOCITY MAPPING (LIST SEPARATELY IN ADDITION TO CODES FOR ECHOCARDIOGRAPHY)
Source: CMS coverage guidance
CPT 92250high
FUNDUS PHOTOGRAPHY WITH INTERPRETATION AND REPORT
Source: CMS coverage guidance
CPT 92227high
IMAGING OF RETINA FOR DETECTION OR MONITORING OF DISEASE; WITH REMOTE CLINICAL STAFF REVIEW AND REPORT, UNILATERAL OR BILATERAL
Source: CMS coverage guidance
CPT 92228high
IMAGING OF RETINA FOR DETECTION OR MONITORING OF DISEASE; WITH REMOTE PHYSICIAN OR OTHER QUALIFIED HEALTH CARE PROFESSIONAL INTERPRETATION AND REPORT, UNILATERAL OR BILATERAL
Source: CMS coverage guidance
CPT 92202high
OPHTHALMOSCOPY, EXTENDED; WITH DRAWING OF OPTIC NERVE OR MACULA (EG, FOR GLAUCOMA, MACULAR PATHOLOGY, TUMOR) WITH INTERPRETATION AND REPORT, UNILATERAL OR BILATERAL
Source: CMS coverage guidance
CPT 92201high
OPHTHALMOSCOPY, EXTENDED; WITH RETINAL DRAWING AND SCLERAL DEPRESSION OF PERIPHERAL RETINAL DISEASE (EG, FOR RETINAL TEAR, RETINAL DETACHMENT, RETINAL TUMOR) WITH INTERPRETATION AND REPORT, UNILATERAL OR BILATERAL
Source: CMS coverage guidance

Coding guidelines

Common synonyms

Marfan syndrome with ocular manifestations

Frequently asked questions

Code details

CodeQ87.42
SystemICD10
Display nameMarfan syndrome with ocular manifestations
ChapterCongenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA0)
BlockOther congenital malformations

Flags

BillableYes
Valid clinical useYes

Source

SourceICD-10
Version2026-annual
Releaseannual
Year2026

Index terms

Matched terms
Syndrome

About this content

This page is prepared by HealthAssure's clinical team using official coding standards from ICD-10. AI tools assist with drafting explanations, which are then reviewed and verified by healthcare professionals for accuracy. This content is for informational purposes and does not replace professional medical advice. Meet our team.

ICD-10 Code Q87.42 for Marfan syndrome with ocular manifestations | HealthAssure