ICD10BillableValid for clinical use

ICD-10 Code Q99.1: 46, XX true hermaphrodite

Q99.1 is a billable ICD-10 diagnosis code used to classify 46, XX true hermaphrodite in medical records and claims. You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records. ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA0).

Reviewed by HealthAssure Clinical TeamUpdated 26 May 2026

What is this code?

ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA0).

When is it used?

  • May be used when a clinician documents 46, xx true hermaphrodite in a patient's medical record.
  • May appear in hospital records, claims, referrals, and clinical documentation.
  • This code can be used as a clinically usable diagnosis entry in standardized coding workflows.

What it does not mean

  • A code alone does not explain severity, treatment plan, or outcome.
  • A medical code should not be treated as a substitute for a doctor's diagnosis or advice.

Code hierarchy

chapter
17Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA0)
block
Q90-Q99Chromosomal abnormalities, not elsewhere classified
category
Q99Other chromosome abnormalities, not elsewhere classified
currentQ99

Official coding notes

Inclusion terms
  • 46, XX with streak gonads
  • 46, XY with streak gonads
  • Pure gonadal dysgenesis

Where you may see this code

You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records.

Coding guidelines

Compatibility

Legacy and official ICD code match exactly.
Legacy codes
Q99.1

Common synonyms

46, XX true hermaphrodite

Frequently asked questions

Code details

CodeQ99.1
SystemICD10
Display name46, XX true hermaphrodite
ChapterCongenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA0)
BlockChromosomal abnormalities, not elsewhere classified

Flags

BillableYes
Valid clinical useYes

Source

SourceICD-10
Version2026-annual
Releaseannual
Year2026

Index terms

Matched terms
Anomaly, anomalous(congenital) (unspecified type)DysgenesisHermaphrodite, hermaphroditism(true)Hermaphrodite, hermaphroditism(true)KaryotypeKaryotypeSwyer syndromeSyndrome

About this content

This page is prepared by HealthAssure's clinical team using official coding standards from ICD-10. AI tools assist with drafting explanations, which are then reviewed and verified by healthcare professionals for accuracy. This content is for informational purposes and does not replace professional medical advice. Meet our team.

ICD-10 Code Q99.1 for 46, XX true hermaphrodite | HealthAssure