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ICD10

ICD-10 Code A81.0: Creutzfeldt-Jakob disease

A81.0 is an ICD-10 diagnosis entry used to group records related to Creutzfeldt-Jakob disease. You may see this entry in coding references, medical records, or claims workflows when a broader diagnosis category is being reviewed before a more specific code is chosen. ICD-10 entries help standardize how diagnoses are organized for coding, reporting, analytics, and documentation. This code sits within the broader ICD-10 area for Certain infectious and parasitic diseases (A00-B99).

What is this code?

ICD-10 entries help standardize how diagnoses are organized for coding, reporting, analytics, and documentation. This code sits within the broader ICD-10 area for Certain infectious and parasitic diseases (A00-B99).

When is it used?

  • May be used when a clinician documents creutzfeldt-jakob disease in a patient's medical record.
  • May appear in hospital records, claims, referrals, and clinical documentation.
  • This code may act more like a grouping or parent code, so a more specific child code may be used in final documentation when available.

What it does not mean

  • A code alone does not explain severity, treatment plan, or outcome.
  • A medical code should not be treated as a substitute for a doctor's diagnosis or advice.
  • This entry may represent a broader category rather than the most specific billable code.

Code hierarchy

chapter
1Certain infectious and parasitic diseases (A00-B99)
block
A80-A89Viral and prion infections of the central nervous system
category
A81Atypical virus infections of central nervous system
currentA81

Where you may see this code

You may see this entry in coding references, medical records, or claims workflows when a broader diagnosis category is being reviewed before a more specific code is chosen.

Related specialists

Infectious Disease SpecialistGeneral Physician

Coding guidelines

Compatibility

Legacy code aligns to an official FY 2026 category. Frontend should resolve to the official category page and surface the billable child codes.
Legacy codes
A81.0
Replacement codes
A81.00 — Creutzfeldt-Jakob disease, unspecifiedA81.01 — Variant Creutzfeldt-Jakob diseaseA81.09 — Other Creutzfeldt-Jakob disease

Common synonyms

Creutzfeldt-Jakob disease

Frequently asked questions

Code details

CodeA81.0
SystemICD10
Display nameCreutzfeldt-Jakob disease
ChapterCertain infectious and parasitic diseases (A00-B99)
BlockViral and prion infections of the central nervous system

Flags

BillableNo
Valid clinical useNo

Source

SourceICD-10
Version2026-annual
Releaseannual
Year2026

About this content

This page is prepared by HealthAssure's clinical team using official coding standards from ICD-10. AI tools assist with drafting explanations, which are then reviewed and verified by healthcare professionals for accuracy. This content is for informational purposes and does not replace professional medical advice. Meet our team.