What does ICD-10 code E00 mean?

ICD-10 code E00 is the standardized code used for congenital iodine-deficiency syndrome in medical records and coding systems.

When is ICD-10 code E00 used?

Doctors, hospitals, and insurers may use ICD-10 code E00 when recording congenital iodine-deficiency syndrome in a standardized format. This entry may also act as a broader category that points toward more specific child codes.

Does ICD-10 code E00 confirm a diagnosis?

No. A code helps standardize documentation and claims, but it should not be read as a substitute for a clinician's full assessment.

ICD10

ICD-10 Code E00: Congenital iodine-deficiency syndrome

Name: ICD-10 Code E00: Congenital iodine-deficiency syndrome
Creator: HealthAssure Clinical Team
Published: 2026-05-21T06:04:41.313Z

E00 is an ICD-10 diagnosis entry used to group records related to Congenital iodine-deficiency syndrome. You may see this entry in coding references, medical records, or claims workflows when a broader diagnosis category is being reviewed before a more specific code is chosen. ICD-10 entries help standardize how diagnoses are organized for coding, reporting, analytics, and documentation. This code sits within the broader ICD-10 area for Endocrine, nutritional and metabolic diseases (E00-E89).

Reviewed by HealthAssure Clinical TeamUpdated 21 May 2026

What is this code?

ICD-10 entries help standardize how diagnoses are organized for coding, reporting, analytics, and documentation. This code sits within the broader ICD-10 area for Endocrine, nutritional and metabolic diseases (E00-E89).

When is it used?

May be used when a clinician documents congenital iodine-deficiency syndrome in a patient's medical record.
May appear in hospital records, claims, referrals, and clinical documentation.
This code may act more like a grouping or parent code, so a more specific child code may be used in final documentation when available.

What it does not mean

A code alone does not explain severity, treatment plan, or outcome.
A medical code should not be treated as a substitute for a doctor's diagnosis or advice.
This entry may represent a broader category rather than the most specific billable code.

Code hierarchy

chapter

4Endocrine, nutritional and metabolic diseases (E00-E89)

block

E00-E07Disorders of thyroid gland

currentE00-E07

Official coding notes

Applicable to

code (F70-F79) to identify associated intellectual disabilities.

Excludes1 (do not code together)

subclinical iodine-deficiency hypothyroidism (E02)

Use additional code

code (F70-F79) to identify associated intellectual disabilities.

Where you may see this code

You may see this entry in coding references, medical records, or claims workflows when a broader diagnosis category is being reviewed before a more specific code is chosen.

Related specialists

EndocrinologistGeneral Physician

Sibling codes

E01Iodine-deficiency related thyroid disorders and allied conditions E02Subclinical iodine-deficiency hypothyroidismbillable E03Other hypothyroidism E04Other nontoxic goiter E05Thyrotoxicosis [hyperthyroidism]E06Thyroiditis E07Other disorders of thyroid

Coding guidelines

Compatibility

Legacy code aligns to an official FY 2026 category. Frontend should resolve to the official category page and surface the billable child codes.

Legacy codes

E00

Replacement codes

E00.0 — Congenital iodine-deficiency syndrome, neurological typeE00.1 — Congenital iodine-deficiency syndrome, myxedematous typeE00.2 — Congenital iodine-deficiency syndrome, mixed typeE00.9 — Congenital iodine-deficiency syndrome, unspecified

Common synonyms

Congenital iodine-deficiency syndrome

Frequently asked questions

About this content

This page is prepared by HealthAssure's clinical team using official coding standards from ICD-10. AI tools assist with drafting explanations, which are then reviewed and verified by healthcare professionals for accuracy. This content is for informational purposes and does not replace professional medical advice. Meet our team.