ICD10BillableValid for clinical use
ICD-10 Code E25.0: Congenital adrenogenital disorders associated with enzyme deficiency
Reviewed by HealthAssure Clinical TeamUpdated 26 May 2026
What is this code?
ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Endocrine, nutritional and metabolic diseases (E00-E89).
When is it used?
- May be used when a clinician documents congenital adrenogenital disorders associated with enzyme deficiency in a patient's medical record.
- May appear in hospital records, claims, referrals, and clinical documentation.
- This code can be used as a clinically usable diagnosis entry in standardized coding workflows.
What it does not mean
- A code alone does not explain severity, treatment plan, or outcome.
- A medical code should not be treated as a substitute for a doctor's diagnosis or advice.
Code hierarchy
chapter
4Endocrine, nutritional and metabolic diseases (E00-E89)
block
E20-E35Disorders of other endocrine glands
category
E25Adrenogenital disorders
currentE25
Official coding notes
Inclusion terms
- Congenital adrenal hyperplasia
- 21-Hydroxylase deficiency
- Salt-losing congenital adrenal hyperplasia
Where you may see this code
You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records.
Related specialists
EndocrinologistGeneral Physician
Sibling codes
Coverage-related procedures and services
CPT 00532high
ANESTHESIA FOR ACCESS TO CENTRAL VENOUS CIRCULATION
Source: CMS coverage guidance
CPT 01420high
ANESTHESIA FOR ALL CAST APPLICATIONS, REMOVAL, OR REPAIR INVOLVING KNEE JOINT
Source: CMS coverage guidance
CPT 01730high
ANESTHESIA FOR ALL CLOSED PROCEDURES ON HUMERUS AND ELBOW
Source: CMS coverage guidance
CPT 01380high
ANESTHESIA FOR ALL CLOSED PROCEDURES ON KNEE JOINT
Source: CMS coverage guidance
CPT 01820high
ANESTHESIA FOR ALL CLOSED PROCEDURES ON RADIUS, ULNA, WRIST, OR HAND BONES
Source: CMS coverage guidance
CPT 00322high
ANESTHESIA FOR ALL PROCEDURES ON ESOPHAGUS, THYROID, LARYNX, TRACHEA AND LYMPHATIC SYSTEM OF NECK; NEEDLE BIOPSY OF THYROID
Source: CMS coverage guidance
Mapped diagnoses and classifications
SNOMED_CT 49013001high
17 alpha-Hydroxyprogesterone aldolase deficiency
Source: SNOMED International ICD-10 map
SNOMED_CT 54470008high
3 beta-Hydroxysteroid dehydrogenase deficiency
Source: SNOMED International ICD-10 map
SNOMED_CT 237755009high
CAH - desmolase deficiency
Source: SNOMED International ICD-10 map
SNOMED_CT 44231009high
Cholesterol monooxygenase (side-chain cleaving) deficiency
Source: SNOMED International ICD-10 map
SNOMED_CT 717261006high
Classic congenital adrenal hyperplasia due to 21-hydroxylase deficiency
Source: SNOMED International ICD-10 map
SNOMED_CT 237751000high
Congenital adrenal hyperplasia
Source: SNOMED International ICD-10 map
Coding guidelines
Compatibility
Legacy and official ICD code match exactly.
Legacy codes
E25.0
Common synonyms
Congenital adrenogenital disorders associated with enzyme deficiency
Frequently asked questions
About this content
This page is prepared by HealthAssure's clinical team using official coding standards from ICD-10. AI tools assist with drafting explanations, which are then reviewed and verified by healthcare professionals for accuracy. This content is for informational purposes and does not replace professional medical advice. Meet our team.