When is ICD-10 code E71.310 used?

Doctors, hospitals, and insurers may use ICD-10 code E71.310 when recording long chain/very long chain acyl coa dehydrogenase deficiency in a standardized format.

Does ICD-10 code E71.310 confirm a diagnosis?

No. A code helps standardize documentation and claims, but it should not be read as a substitute for a clinician's full assessment.

ICD10BillableValid for clinical use

ICD-10 Code E71.310: Long chain/very long chain acyl CoA dehydrogenase deficiency

Name: ICD-10 Code E71.310: Long chain/very long chain acyl CoA dehydrogenase deficiency
Creator: HealthAssure Clinical Team
Published: 2026-05-21T06:05:21.349Z

E71.310 is a billable ICD-10 diagnosis code used to classify Long chain/very long chain acyl CoA dehydrogenase deficiency in medical records and claims. You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records. ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Endocrine, nutritional and metabolic diseases (E00-E89).

Reviewed by HealthAssure Clinical TeamUpdated 21 May 2026

What is this code?

ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Endocrine, nutritional and metabolic diseases (E00-E89).

When is it used?

May be used when a clinician documents long chain/very long chain acyl coa dehydrogenase deficiency in a patient's medical record.
May appear in hospital records, claims, referrals, and clinical documentation.
This code can be used as a clinically usable diagnosis entry in standardized coding workflows.

What it does not mean

A code alone does not explain severity, treatment plan, or outcome.
A medical code should not be treated as a substitute for a doctor's diagnosis or advice.

Code hierarchy

chapter

4Endocrine, nutritional and metabolic diseases (E00-E89)

block

E70-E88Metabolic disorders

Official coding notes

Inclusion terms

LCAD deficiency
VLCAD deficiency

Where you may see this code

You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records.

Related specialists

EndocrinologistGeneral Physician

Sibling codes

E71.311Medium chain acyl CoA dehydrogenase deficiencybillable E71.312Short chain acyl CoA dehydrogenase deficiencybillable E71.313Glutaric aciduria type IIbillable E71.314Muscle carnitine palmitoyltransferase deficiencybillable E71.318Other disorders of fatty-acid oxidationbillable

Coding guidelines

Common synonyms

Long chain/very long chain acyl CoA dehydrogenase deficiency

Frequently asked questions

About this content

This page is prepared by HealthAssure's clinical team using official coding standards from ICD-10. AI tools assist with drafting explanations, which are then reviewed and verified by healthcare professionals for accuracy. This content is for informational purposes and does not replace professional medical advice. Meet our team.