What does ICD-10 code E71.313 mean?

ICD-10 code E71.313 is the standardized code used for glutaric aciduria type ii in medical records and coding systems.

When is ICD-10 code E71.313 used?

Doctors, hospitals, and insurers may use ICD-10 code E71.313 when recording glutaric aciduria type ii in a standardized format.

Does ICD-10 code E71.313 confirm a diagnosis?

No. A code helps standardize documentation and claims, but it should not be read as a substitute for a clinician's full assessment.

ICD10BillableValid for clinical use

ICD-10 Code E71.313: Glutaric aciduria type II

Name: ICD-10 Code E71.313: Glutaric aciduria type II
Creator: HealthAssure Clinical Team
Published: 2026-05-21T06:05:21.474Z

E71.313 is a billable ICD-10 diagnosis code used to classify Glutaric aciduria type II in medical records and claims. You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records. ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Endocrine, nutritional and metabolic diseases (E00-E89).

Reviewed by HealthAssure Clinical TeamUpdated 21 May 2026

What is this code?

ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Endocrine, nutritional and metabolic diseases (E00-E89).

When is it used?

May be used when a clinician documents glutaric aciduria type ii in a patient's medical record.
May appear in hospital records, claims, referrals, and clinical documentation.
This code can be used as a clinically usable diagnosis entry in standardized coding workflows.

What it does not mean

A code alone does not explain severity, treatment plan, or outcome.
A medical code should not be treated as a substitute for a doctor's diagnosis or advice.

Code hierarchy

chapter

4Endocrine, nutritional and metabolic diseases (E00-E89)

block

E70-E88Metabolic disorders

Official coding notes

Inclusion terms

Glutaric aciduria type II A
Glutaric aciduria type II B
Glutaric aciduria type II C

Excludes1 (do not code together)

glutaric aciduria (type 1) NOS (E72.3)

Where you may see this code

You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records.

Related specialists

EndocrinologistGeneral Physician

Sibling codes

E71.310Long chain/very long chain acyl CoA dehydrogenase deficiencybillable E71.311Medium chain acyl CoA dehydrogenase deficiencybillable E71.312Short chain acyl CoA dehydrogenase deficiencybillable E71.314Muscle carnitine palmitoyltransferase deficiencybillable E71.318Other disorders of fatty-acid oxidationbillable

Coding guidelines

Common synonyms

Glutaric aciduria type II

Frequently asked questions

About this content

This page is prepared by HealthAssure's clinical team using official coding standards from ICD-10. AI tools assist with drafting explanations, which are then reviewed and verified by healthcare professionals for accuracy. This content is for informational purposes and does not replace professional medical advice. Meet our team.