ICD10BillableValid for clinical use
ICD-10 Code E72.3: Disorders of lysine and hydroxylysine metabolism
Reviewed by HealthAssure Clinical TeamUpdated 26 May 2026
What is this code?
ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Endocrine, nutritional and metabolic diseases (E00-E89).
When is it used?
- May be used when a clinician documents disorders of lysine and hydroxylysine metabolism in a patient's medical record.
- May appear in hospital records, claims, referrals, and clinical documentation.
- This code can be used as a clinically usable diagnosis entry in standardized coding workflows.
What it does not mean
- A code alone does not explain severity, treatment plan, or outcome.
- A medical code should not be treated as a substitute for a doctor's diagnosis or advice.
Code hierarchy
chapter
4Endocrine, nutritional and metabolic diseases (E00-E89)
block
E70-E88Metabolic disorders
category
E72Other disorders of amino-acid metabolism
currentE72
Official coding notes
Inclusion terms
- Glutaric aciduria NOS
- Glutaric aciduria (type I)
- Hydroxylysinemia
- Hyperlysinemia
Excludes1 (do not code together)
- glutaric aciduria type II (E71.313)
- Refsum's disease (G60.1)
- Zellweger syndrome (E71.510)
Where you may see this code
You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records.
Related specialists
EndocrinologistGeneral Physician
Related codes
E72.0Disorders of amino-acid transportcategoryE72.1Disorders of sulfur-bearing amino-acid metabolismcategoryE72.2Disorders of urea cycle metabolismcategoryE72.4Disorders of ornithine metabolismcodeE72.5Disorders of glycine metabolismcategoryE72.8Other specified disorders of amino-acid metabolismcategoryE72.9Disorder of amino-acid metabolism, unspecifiedcode
Sibling codes
E72.0Disorders of amino-acid transportE72.1Disorders of sulfur-bearing amino-acid metabolismE72.2Disorders of urea cycle metabolismE72.4Disorders of ornithine metabolismbillableE72.5Disorders of glycine metabolismE72.8Other specified disorders of amino-acid metabolismE72.9Disorder of amino-acid metabolism, unspecifiedbillable
Mapped diagnoses and classifications
SNOMED_CT 237931009high
2-Ketoadipic acidemia
Source: SNOMED International ICD-10 map
SNOMED_CT 782918002high
2-aminoadipic 2-oxoadipic aciduria
Source: SNOMED International ICD-10 map
SNOMED_CT 698870008high
2-hydroxyglutaric aciduria
Source: SNOMED International ICD-10 map
SNOMED_CT 237960000high
D-2(OH) glutaric aciduria
Source: SNOMED International ICD-10 map
SNOMED_CT 50056009high
Dibasic amino aciduria type 1
Source: SNOMED International ICD-10 map
SNOMED_CT 77402005high
Disorder of lysine AND/OR hydroxylysine metabolism
Source: SNOMED International ICD-10 map
Coding guidelines
Compatibility
Legacy and official ICD code match exactly.
Legacy codes
E72.3
Common synonyms
Disorders of lysine and hydroxylysine metabolism
Frequently asked questions
About this content
This page is prepared by HealthAssure's clinical team using official coding standards from ICD-10. AI tools assist with drafting explanations, which are then reviewed and verified by healthcare professionals for accuracy. This content is for informational purposes and does not replace professional medical advice. Meet our team.