ICD10BillableValid for clinical use
ICD-10 Code G90.1: Familial dysautonomia [Riley-Day]
Reviewed by HealthAssure Clinical TeamUpdated 26 May 2026
What is this code?
ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Diseases of the nervous system (G00-G99).
When is it used?
- May be used when a clinician documents familial dysautonomia [riley-day] in a patient's medical record.
- May appear in hospital records, claims, referrals, and clinical documentation.
- This code can be used as a clinically usable diagnosis entry in standardized coding workflows.
What it does not mean
- A code alone does not explain severity, treatment plan, or outcome.
- A medical code should not be treated as a substitute for a doctor's diagnosis or advice.
Code hierarchy
chapter
6Diseases of the nervous system (G00-G99)
block
G89-G99Other disorders of the nervous system
category
G90Disorders of autonomic nervous system
currentG90
Where you may see this code
You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records.
Related specialists
NeurologistGeneral Physician
Related codes
G90.0Idiopathic peripheral autonomic neuropathycategoryG90.2Horner's syndromecodeG90.3Multi-system degeneration of the autonomic nervous systemcodeG90.4Autonomic dysreflexiacodeG90.5Complex regional pain syndrome I (CRPS I)categoryG90.8Other disorders of autonomic nervous systemcategoryG90.9Disorder of the autonomic nervous system, unspecifiedcodeG90.APostural orthostatic tachycardia syndrome [POTS]codeG90.BLMNB1-related autosomal dominant leukodystrophycode
Sibling codes
G90.0Idiopathic peripheral autonomic neuropathyG90.2Horner's syndromebillableG90.3Multi-system degeneration of the autonomic nervous systembillableG90.4Autonomic dysreflexiabillableG90.5Complex regional pain syndrome I (CRPS I)G90.8Other disorders of autonomic nervous systemG90.9Disorder of the autonomic nervous system, unspecifiedbillableG90.APostural orthostatic tachycardia syndrome [POTS]billableG90.BLMNB1-related autosomal dominant leukodystrophybillable
Coverage-related procedures and services
CPT 70460high
COMPUTED TOMOGRAPHY, HEAD OR BRAIN; WITH CONTRAST MATERIAL(S)
Source: CMS coverage guidance
CPT 70450high
COMPUTED TOMOGRAPHY, HEAD OR BRAIN; WITHOUT CONTRAST MATERIAL
Source: CMS coverage guidance
CPT 70470high
COMPUTED TOMOGRAPHY, HEAD OR BRAIN; WITHOUT CONTRAST MATERIAL, FOLLOWED BY CONTRAST MATERIAL(S) AND FURTHER SECTIONS
Source: CMS coverage guidance
CPT 96105high
ASSESSMENT OF APHASIA (INCLUDES ASSESSMENT OF EXPRESSIVE AND RECEPTIVE SPEECH AND LANGUAGE FUNCTION, LANGUAGE COMPREHENSION, SPEECH PRODUCTION ABILITY, READING, SPELLING, WRITING, EG, BY BOSTON DIAGNOSTIC APHASIA EXAMINATION) WITH INTERPRETATION AND REPORT, PER HOUR
Source: CMS coverage guidance
CPT 92524high
BEHAVIORAL AND QUALITATIVE ANALYSIS OF VOICE AND RESONANCE
Source: CMS coverage guidance
CPT 72126high
COMPUTED TOMOGRAPHY, CERVICAL SPINE; WITH CONTRAST MATERIAL
Source: CMS coverage guidance
Mapped diagnoses and classifications
Coding guidelines
Compatibility
Legacy and official ICD code match exactly.
Legacy codes
G90.1
Common synonyms
Familial dysautonomia [Riley-Day]
Frequently asked questions
About this content
This page is prepared by HealthAssure's clinical team using official coding standards from ICD-10. AI tools assist with drafting explanations, which are then reviewed and verified by healthcare professionals for accuracy. This content is for informational purposes and does not replace professional medical advice. Meet our team.