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ICD10BillableValid for clinical use

ICD-10 Code I27.0: Primary pulmonary hypertension

I27.0 is a billable ICD-10 diagnosis code used to classify Primary pulmonary hypertension in medical records and claims. You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records. ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Diseases of the circulatory system (I00-I99).

Reviewed by HealthAssure Clinical TeamUpdated 26 May 2026

What is this code?

ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Diseases of the circulatory system (I00-I99).

When is it used?

  • May be used when a clinician documents primary pulmonary hypertension in a patient's medical record.
  • May appear in hospital records, claims, referrals, and clinical documentation.
  • This code can be used as a clinically usable diagnosis entry in standardized coding workflows.

What it does not mean

  • A code alone does not explain severity, treatment plan, or outcome.
  • A medical code should not be treated as a substitute for a doctor's diagnosis or advice.

Code hierarchy

chapter
9Diseases of the circulatory system (I00-I99)
block
I26-I28Pulmonary heart disease and diseases of pulmonary circulation
category
I27Other pulmonary heart diseases
currentI27

Official coding notes

Inclusion terms
  • Heritable pulmonary arterial hypertension
  • Idiopathic pulmonary arterial hypertension
  • Primary group 1 pulmonary hypertension
  • Primary pulmonary arterial hypertension
Excludes1 (do not code together)
  • persistent pulmonary hypertension of newborn (P29.30)
  • pulmonary hypertension NOS (I27.20)
  • secondary pulmonary arterial hypertension (I27.21)
  • secondary pulmonary hypertension (I27.29)

Where you may see this code

You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records.

Related specialists

CardiologistGeneral Physician

Coverage-related procedures and services

CPT 93350high
ECHOCARDIOGRAPHY, TRANSTHORACIC, REAL-TIME WITH IMAGE DOCUMENTATION (2D), INCLUDES M-MODE RECORDING, WHEN PERFORMED, DURING REST AND CARDIOVASCULAR STRESS TEST USING TREADMILL, BICYCLE EXERCISE AND/OR PHARMACOLOGICALLY INDUCED STRESS, WITH INTERPRETATION AND REPORT;
Source: CMS coverage guidance
CPT 93351high
ECHOCARDIOGRAPHY, TRANSTHORACIC, REAL-TIME WITH IMAGE DOCUMENTATION (2D), INCLUDES M-MODE RECORDING, WHEN PERFORMED, DURING REST AND CARDIOVASCULAR STRESS TEST USING TREADMILL, BICYCLE EXERCISE AND/OR PHARMACOLOGICALLY INDUCED STRESS, WITH INTERPRETATION AND REPORT; INCLUDING PERFORMANCE OF CONTINUOUS ELECTROCARDIOGRAPHIC MONITORING, WITH SUPERVISION BY A PHYSICIAN OR OTHER QUALIFIED HEALTH CARE PROFESSIONAL
Source: CMS coverage guidance
CPT 93352high
USE OF ECHOCARDIOGRAPHIC CONTRAST AGENT DURING STRESS ECHOCARDIOGRAPHY (LIST SEPARATELY IN ADDITION TO CODE FOR PRIMARY PROCEDURE)
Source: CMS coverage guidance
CPT 75574high
COMPUTED TOMOGRAPHIC ANGIOGRAPHY, HEART, CORONARY ARTERIES AND BYPASS GRAFTS (WHEN PRESENT), WITH CONTRAST MATERIAL, INCLUDING 3D IMAGE POSTPROCESSING (INCLUDING EVALUATION OF CARDIAC STRUCTURE AND MORPHOLOGY, ASSESSMENT OF CARDIAC FUNCTION, AND EVALUATION OF VENOUS STRUCTURES, IF PERFORMED)
Source: CMS coverage guidance
CPT 75572high
COMPUTED TOMOGRAPHY, HEART, WITH CONTRAST MATERIAL, FOR EVALUATION OF CARDIAC STRUCTURE AND MORPHOLOGY (INCLUDING 3D IMAGE POSTPROCESSING, ASSESSMENT OF CARDIAC FUNCTION, AND EVALUATION OF VENOUS STRUCTURES, IF PERFORMED)
Source: CMS coverage guidance
CPT 75573high
COMPUTED TOMOGRAPHY, HEART, WITH CONTRAST MATERIAL, FOR EVALUATION OF CARDIAC STRUCTURE AND MORPHOLOGY IN THE SETTING OF CONGENITAL HEART DISEASE (INCLUDING 3D IMAGE POSTPROCESSING, ASSESSMENT OF LEFT VENTRICULAR [LV] CARDIAC FUNCTION, RIGHT VENTRICULAR [RV] STRUCTURE AND FUNCTION AND EVALUATION OF VASCULAR STRUCTURES, IF PERFORMED)
Source: CMS coverage guidance

Coding guidelines

Compatibility

Legacy and official ICD code match exactly.
Legacy codes
I27.0

Common synonyms

Primary pulmonary hypertension

Frequently asked questions

Code details

CodeI27.0
SystemICD10
Display namePrimary pulmonary hypertension
ChapterDiseases of the circulatory system (I00-I99)
BlockPulmonary heart disease and diseases of pulmonary circulation

Flags

BillableYes
Valid clinical useYes

Source

SourceICD-10
Version2026-annual
Releaseannual
Year2026

Index terms

Matched terms
Arrillaga-Ayerza syndrome(pulmonary sclerosis with pulmonary hypertension)Arteriosclerosis, arteriosclerotic(diffuse) (obliterans) (of) (senile) (with calcification)Ayerza's disease or syndrome(pulmonary artery sclerosis with pulmonary hypertension)Cardiopathia nigraDisease, diseasedDisease, diseasedDisease, diseasedHypertension, hypertensive(accelerated) (benign) (essential) (idiopathic) (malignant) (systemic)Hypertension, hypertensive(accelerated) (benign) (essential) (idiopathic) (malignant) (systemic)Sclerosis, scleroticSyndromeSyndrome

About this content

This page is prepared by HealthAssure's clinical team using official coding standards from ICD-10. AI tools assist with drafting explanations, which are then reviewed and verified by healthcare professionals for accuracy. This content is for informational purposes and does not replace professional medical advice. Meet our team.

ICD-10 Code I27.0 for Primary pulmonary hypertension | HealthAssure