ICD10BillableValid for clinical use
ICD-10 Code I27.1: Kyphoscoliotic heart disease
Reviewed by HealthAssure Clinical TeamUpdated 26 May 2026
What is this code?
ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Diseases of the circulatory system (I00-I99).
đź“‹Clinical overview
This ICD-10 code is commonly used when documentation describes pulmonary hypertension. The most accurate code depends on whether the condition is primary or secondary and whether the chart identifies a left-heart, lung-and-hypoxia, chronic-thromboembolic, or other driving mechanism.
When is it used?
- May be used when a clinician documents kyphoscoliotic heart disease in a patient's medical record.
- May appear in hospital records, claims, referrals, and clinical documentation.
- This code can be used as a clinically usable diagnosis entry in standardized coding workflows.
What it does not mean
- A code alone does not explain severity, treatment plan, or outcome.
- A medical code should not be treated as a substitute for a doctor's diagnosis or advice.
đź©şClinical context
When commonly used
- Cardiology, pulmonology, inpatient, and utilization-review workflows where pulmonary hypertension affects evaluation, treatment planning, or chronic disease follow-up.
- Coding workflows where the chart identifies primary versus secondary pulmonary hypertension or names the underlying mechanism that changes final code specificity.
Common management context
- Evaluation often includes echocardiography, cardiopulmonary assessment, imaging review, hemodynamic context, and follow-up of the underlying heart, lung, or thromboembolic condition.
- Documentation usually becomes more specific when the chart identifies primary pulmonary hypertension, secondary pulmonary arterial hypertension, left-heart-disease association, lung-disease or hypoxia association, chronic thromboembolic disease, or another secondary pattern.
- Specialist context already linked on this page includes Cardiologist, General Physician, ENT Specialist.
🔍Key distinctions
Important notes
- This ICD-10 family captures pulmonary-hypertension diagnoses rather than systemic hypertension or unrelated pulmonary disorders without pulmonary-hypertension context.
- Primary versus secondary disease and the documented underlying mechanism both affect final code specificity inside this family.
Related codes to consider
I27.0Primary pulmonary hypertension
Related pulmonary-hypertension ICD-10 code; documentation often becomes more specific when the chart identifies primary versus secondary disease or names the heart, lung, hypoxia, or thromboembolic mechanism.
I27.2Other secondary pulmonary hypertension
Related pulmonary-hypertension ICD-10 code; documentation often becomes more specific when the chart identifies primary versus secondary disease or names the heart, lung, hypoxia, or thromboembolic mechanism.
I27.8Other specified pulmonary heart diseases
Related pulmonary-hypertension ICD-10 code; documentation often becomes more specific when the chart identifies primary versus secondary disease or names the heart, lung, hypoxia, or thromboembolic mechanism.
I27.9Pulmonary heart disease, unspecified
Related pulmonary-hypertension ICD-10 code; documentation often becomes more specific when the chart identifies primary versus secondary disease or names the heart, lung, hypoxia, or thromboembolic mechanism.
Code hierarchy
chapter
9Diseases of the circulatory system (I00-I99)
block
I26-I28Pulmonary heart disease and diseases of pulmonary circulation
category
I27Other pulmonary heart diseases
currentI27
Where you may see this code
You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records.
Related specialists
CardiologistGeneral PhysicianENT Specialist
Related codes
Sibling codes
Coverage-related procedures and services
CPT 93319high
3D ECHOCARDIOGRAPHIC IMAGING AND POSTPROCESSING DURING TRANSESOPHAGEAL ECHOCARDIOGRAPHY, OR DURING TRANSTHORACIC ECHOCARDIOGRAPHY FOR CONGENITAL CARDIAC ANOMALIES, FOR THE ASSESSMENT OF CARDIAC STRUCTURE(S) (EG, CARDIAC CHAMBERS AND VALVES, LEFT ATRIAL APPENDAGE, INTERATRIAL SEPTUM, INTERVENTRICULAR SEPTUM) AND FUNCTION, WHEN PERFORMED (LIST SEPARATELY IN ADDITION TO CODE FOR ECHOCARDIOGRAPHIC IMAGING)
Source: CMS coverage guidance
CPT 76376high
3D RENDERING WITH INTERPRETATION AND REPORTING OF COMPUTED TOMOGRAPHY, MAGNETIC RESONANCE IMAGING, ULTRASOUND, OR OTHER TOMOGRAPHIC MODALITY WITH IMAGE POSTPROCESSING UNDER CONCURRENT SUPERVISION; NOT REQUIRING IMAGE POSTPROCESSING ON AN INDEPENDENT WORKSTATION
Source: CMS coverage guidance
CPT 76377high
3D RENDERING WITH INTERPRETATION AND REPORTING OF COMPUTED TOMOGRAPHY, MAGNETIC RESONANCE IMAGING, ULTRASOUND, OR OTHER TOMOGRAPHIC MODALITY WITH IMAGE POSTPROCESSING UNDER CONCURRENT SUPERVISION; REQUIRING IMAGE POSTPROCESSING ON AN INDEPENDENT WORKSTATION
Source: CMS coverage guidance
CPT 94642high
AEROSOL INHALATION OF PENTAMIDINE FOR PNEUMOCYSTIS CARINII PNEUMONIA TREATMENT OR PROPHYLAXIS
Source: CMS coverage guidance
CPT 94728high
AIRWAY RESISTANCE BY OSCILLOMETRY
Source: CMS coverage guidance
CPT 94450high
BREATHING RESPONSE TO HYPOXIA (HYPOXIA RESPONSE CURVE)
Source: CMS coverage guidance
Coding guidelines
Compatibility
Legacy and official ICD code match exactly.
Legacy codes
I27.1
Common synonyms
Kyphoscoliotic heart disease
Frequently asked questions
About this content
This page is prepared by HealthAssure's clinical team using official coding standards from ICD-10. AI tools assist with drafting explanations, which are then reviewed and verified by healthcare professionals for accuracy. This content is for informational purposes and does not replace professional medical advice. Meet our team.