ICD10BillableValid for clinical use
ICD-10 Code G11.0: Congenital nonprogressive ataxia
Reviewed by HealthAssure Clinical TeamUpdated 26 May 2026
What is this code?
ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Diseases of the nervous system (G00-G99).
When is it used?
- May be used when a clinician documents congenital nonprogressive ataxia in a patient's medical record.
- May appear in hospital records, claims, referrals, and clinical documentation.
- This code can be used as a clinically usable diagnosis entry in standardized coding workflows.
What it does not mean
- A code alone does not explain severity, treatment plan, or outcome.
- A medical code should not be treated as a substitute for a doctor's diagnosis or advice.
Code hierarchy
chapter
6Diseases of the nervous system (G00-G99)
block
G10-G14Systemic atrophies primarily affecting the central nervous system
category
G11Hereditary ataxia
currentG11
Where you may see this code
You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records.
Related specialists
NeurologistGeneral Physician
Related codes
G11.1Early-onset cerebellar ataxiacategoryG11.2Late-onset cerebellar ataxiacodeG11.3Cerebellar ataxia with defective DNA repaircodeG11.4Hereditary spastic paraplegiacodeG11.5Hypomyelination - hypogonadotropic hypogonadism - hypodontiacodeG11.6Leukodystrophy with vanishing white matter diseasecodeG11.8Other hereditary ataxiascodeG11.9Hereditary ataxia, unspecifiedcode
Sibling codes
G11.1Early-onset cerebellar ataxiaG11.2Late-onset cerebellar ataxiabillableG11.3Cerebellar ataxia with defective DNA repairbillableG11.4Hereditary spastic paraplegiabillableG11.5Hypomyelination - hypogonadotropic hypogonadism - hypodontiabillableG11.6Leukodystrophy with vanishing white matter diseasebillableG11.8Other hereditary ataxiasbillableG11.9Hereditary ataxia, unspecifiedbillable
Coverage-related procedures and services
HCPCS G0255high
CURRENT PERCEPTION THRESHOLD/SENSORY NERVE CONDUCTION TEST, (SNCT) PER LIMB, ANY NERVE
Source: CMS coverage guidance
CPT 95905high
MOTOR AND/OR SENSORY NERVE CONDUCTION, USING PRECONFIGURED ELECTRODE ARRAY(S), AMPLITUDE AND LATENCY/VELOCITY STUDY, EACH LIMB, INCLUDES F-WAVE STUDY WHEN PERFORMED, WITH INTERPRETATION AND REPORT
Source: CMS coverage guidance
CPT 95907high
NERVE CONDUCTION STUDIES; 1-2 STUDIES
Source: CMS coverage guidance
CPT 95912high
NERVE CONDUCTION STUDIES; 11-12 STUDIES
Source: CMS coverage guidance
CPT 95913high
NERVE CONDUCTION STUDIES; 13 OR MORE STUDIES
Source: CMS coverage guidance
CPT 95908high
NERVE CONDUCTION STUDIES; 3-4 STUDIES
Source: CMS coverage guidance
Mapped diagnoses and classifications
SNOMED_CT 715369006high
Autosomal recessive cerebelloparenchymal disorder type 3
Source: SNOMED International ICD-10 map
SNOMED_CT 717332007high
Cerebellar ataxia Cayman type
Source: SNOMED International ICD-10 map
SNOMED_CT 1177169004high
Congenital cerebellar ataxia due to RNU12 mutation
Source: SNOMED International ICD-10 map
SNOMED_CT 278509004high
Congenital non-progressive ataxia
Source: SNOMED International ICD-10 map
SNOMED_CT 253176002high
Gillespie syndrome
Source: SNOMED International ICD-10 map
SNOMED_CT 785300001high
Infantile-onset autosomal recessive non progressive cerebellar ataxia
Source: SNOMED International ICD-10 map
Coding guidelines
Compatibility
Legacy and official ICD code match exactly.
Legacy codes
G11.0
Common synonyms
Congenital nonprogressive ataxia
Frequently asked questions
About this content
This page is prepared by HealthAssure's clinical team using official coding standards from ICD-10. AI tools assist with drafting explanations, which are then reviewed and verified by healthcare professionals for accuracy. This content is for informational purposes and does not replace professional medical advice. Meet our team.