ICD10BillableValid for clinical use
ICD-10 Code G11.6: Leukodystrophy with vanishing white matter disease
Reviewed by HealthAssure Clinical TeamUpdated 21 May 2026
What is this code?
ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Diseases of the nervous system (G00-G99).
When is it used?
- May be used when a clinician documents leukodystrophy with vanishing white matter disease in a patient's medical record.
- May appear in hospital records, claims, referrals, and clinical documentation.
- This code can be used as a clinically usable diagnosis entry in standardized coding workflows.
What it does not mean
- A code alone does not explain severity, treatment plan, or outcome.
- A medical code should not be treated as a substitute for a doctor's diagnosis or advice.
Code hierarchy
chapter
6Diseases of the nervous system (G00-G99)
block
G10-G14Systemic atrophies primarily affecting the central nervous system
category
G11Hereditary ataxia
currentG11
Where you may see this code
You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records.
Related specialists
NeurologistGeneral Physician
Related codes
G11.0Congenital nonprogressive ataxiacodeG11.1Early-onset cerebellar ataxiacategoryG11.2Late-onset cerebellar ataxiacodeG11.3Cerebellar ataxia with defective DNA repaircodeG11.4Hereditary spastic paraplegiacodeG11.5Hypomyelination - hypogonadotropic hypogonadism - hypodontiacodeG11.8Other hereditary ataxiascodeG11.9Hereditary ataxia, unspecifiedcode
Sibling codes
G11.0Congenital nonprogressive ataxiabillableG11.1Early-onset cerebellar ataxiaG11.2Late-onset cerebellar ataxiabillableG11.3Cerebellar ataxia with defective DNA repairbillableG11.4Hereditary spastic paraplegiabillableG11.5Hypomyelination - hypogonadotropic hypogonadism - hypodontiabillableG11.8Other hereditary ataxiasbillableG11.9Hereditary ataxia, unspecifiedbillable
Coding guidelines
Common synonyms
Leukodystrophy with vanishing white matter disease
Frequently asked questions
About this content
This page is prepared by HealthAssure's clinical team using official coding standards from ICD-10. AI tools assist with drafting explanations, which are then reviewed and verified by healthcare professionals for accuracy. This content is for informational purposes and does not replace professional medical advice. Meet our team.