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ICD10BillableValid for clinical use

ICD-10 Code G11.3: Cerebellar ataxia with defective DNA repair

G11.3 is a billable ICD-10 diagnosis code used to classify Cerebellar ataxia with defective DNA repair in medical records and claims. You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records. ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Diseases of the nervous system (G00-G99).

What is this code?

ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Diseases of the nervous system (G00-G99).

When is it used?

  • May be used when a clinician documents cerebellar ataxia with defective dna repair in a patient's medical record.
  • May appear in hospital records, claims, referrals, and clinical documentation.
  • This code can be used as a clinically usable diagnosis entry in standardized coding workflows.

What it does not mean

  • A code alone does not explain severity, treatment plan, or outcome.
  • A medical code should not be treated as a substitute for a doctor's diagnosis or advice.

Code hierarchy

chapter
6Diseases of the nervous system (G00-G99)
block
G10-G14Systemic atrophies primarily affecting the central nervous system
category
G11Hereditary ataxia
currentG11

Official coding notes

Inclusion terms
  • Ataxia telangiectasia [Louis-Bar]
Excludes2 (may code together if documented)
  • Cockayne's syndrome (Q87.19)
  • other disorders of purine and pyrimidine metabolism (E79.-)
  • xeroderma pigmentosum (Q82.1)

Where you may see this code

You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records.

Related specialists

NeurologistGeneral Physician

Coding guidelines

Compatibility

Legacy and official ICD code match exactly.
Legacy codes
G11.3

Common synonyms

Cerebellar ataxia with defective DNA repair

Frequently asked questions

Code details

CodeG11.3
SystemICD10
Display nameCerebellar ataxia with defective DNA repair
ChapterDiseases of the nervous system (G00-G99)
BlockSystemic atrophies primarily affecting the central nervous system

Flags

BillableYes
Valid clinical useYes

Source

SourceICD-10
Version2026-annual
Releaseannual
Year2026

Index terms

Matched terms
Ataxia, ataxy, ataxicAtaxia, ataxy, ataxicAtaxia-telangiectasia(Louis-Bar)Boder-Sedgwick syndrome(ataxia-telangiectasia)Louis-Bar syndrome(ataxia-telangiectasia)SyndromeSyndromeSyndromeTelangiectasia, telangiectasis(verrucous)

About this content

This page is prepared by HealthAssure's clinical team using official coding standards from ICD-10. AI tools assist with drafting explanations, which are then reviewed and verified by healthcare professionals for accuracy. This content is for informational purposes and does not replace professional medical advice. Meet our team.