HealthAssure
HealthAssureGood Life
ICD10BillableValid for clinical use

ICD-10 Code E78.3: Hyperchylomicronemia

E78.3 is a billable ICD-10 diagnosis code used to classify Hyperchylomicronemia in medical records and claims. You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records. ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Endocrine, nutritional and metabolic diseases (E00-E89).

What is this code?

ICD-10 codes are diagnosis classification codes used in healthcare records, reporting, coding workflows, and billing support. This code sits within the broader ICD-10 area for Endocrine, nutritional and metabolic diseases (E00-E89).

When is it used?

  • May be used when a clinician documents hyperchylomicronemia in a patient's medical record.
  • May appear in hospital records, claims, referrals, and clinical documentation.
  • This code can be used as a clinically usable diagnosis entry in standardized coding workflows.

What it does not mean

  • A code alone does not explain severity, treatment plan, or outcome.
  • A medical code should not be treated as a substitute for a doctor's diagnosis or advice.

Code hierarchy

chapter
4Endocrine, nutritional and metabolic diseases (E00-E89)
block
E70-E88Metabolic disorders
category
E78Disorders of lipoprotein metabolism and other lipidemias
currentE78

Official coding notes

Inclusion terms
  • Chylomicron retention disease
  • Fredrickson's hyperlipoproteinemia, type I or V
  • Hyperlipidemia, group D
  • Mixed hyperglyceridemia

Where you may see this code

You may see this code in hospital records, discharge summaries, insurance claims, encounter documentation, referrals, or other healthcare billing and coding records.

Related specialists

EndocrinologistGeneral Physician

Coding guidelines

Compatibility

Legacy and official ICD code match exactly.
Legacy codes
E78.3

Common synonyms

Hyperchylomicronemia

Frequently asked questions

Code details

CodeE78.3
SystemICD10
Display nameHyperchylomicronemia
ChapterEndocrine, nutritional and metabolic diseases (E00-E89)
BlockMetabolic disorders

Flags

BillableYes
Valid clinical useYes

Source

SourceICD-10
Version2026-annual
Releaseannual
Year2026

Index terms

Matched terms
Bürger-Grütz disease or syndromeChylomicronemia(fasting) (with hyperprebetalipoproteinemia)Disease, diseasedDisease, diseasedFrederickson's hyperlipoproteinemia, typeHepatosplenomegalyHyperchylomicronemia(familial) (primary)Hyperchylomicronemia(familial) (primary)Hyperglyceridemia(endogenous) (essential) (familial) (hereditary) (pure)Hyperlipemia, hyperlipidemiaHyperlipoproteinemiaHyperlipoproteinemia

About this content

This page is prepared by HealthAssure's clinical team using official coding standards from ICD-10. AI tools assist with drafting explanations, which are then reviewed and verified by healthcare professionals for accuracy. This content is for informational purposes and does not replace professional medical advice. Meet our team.